Idh3a (isocitrate dehydrogenase (NAD(+)) 3 catalytic subunit alpha) - Rat Genome Database

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Gene: Idh3a (isocitrate dehydrogenase (NAD(+)) 3 catalytic subunit alpha) Ictidomys tridecemlineatus
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Symbol: Idh3a
Name: isocitrate dehydrogenase (NAD(+)) 3 catalytic subunit alpha
RGD ID: 12586639
Description: ENCODES a protein that exhibits isocitrate dehydrogenase (NAD+) activity (ortholog); INVOLVED IN isocitrate metabolic process (inferred); tricarboxylic acid cycle (inferred); PARTICIPATES IN citric acid cycle pathway; fumaric aciduria pathway; mitochondrial complex II deficiency pathway; ASSOCIATED WITH Bloom syndrome (ortholog); colorectal cancer (ortholog); fundus dystrophy (ortholog); FOUND IN isocitrate dehydrogenase complex (NAD+) (inferred); mitochondrion (inferred)
Type: protein-coding
RefSeq Status: MODEL
Previously known as: isocitrate dehydrogenase (NAD(+)) 3 alpha; isocitrate dehydrogenase 3 (NAD(+)) alpha; isocitrate dehydrogenase [NAD] subunit alpha, mitochondrial
RGD Orthologs
Human
Mouse
Rat
Chinchilla
Bonobo
Dog
Pig
Green Monkey
Naked Mole-Rat
Alliance Orthologs
More Info more info ...
Latest Assembly: SpeTri2.0 - Squirrel SpeTri2.0 Assembly
Position:
Squirrel AssemblyChrPosition (strand)SourceGenome Browsers
JBrowseNCBIUCSCEnsembl
HiC_Itri_2NW_024408640118,974,940 - 118,994,520 (-)NCBIHiC_Itri_2
SpeTri2.0 EnsemblNW_00493647136,822,971 - 36,842,610 (-)EnsemblSpeTri2.0SpeTri2.0 Ensembl
SpeTri2.0NW_00493647136,823,003 - 36,842,576 (-)NCBISpeTri2.0SpeTri2.0SpeTri2.0
JBrowse: View Region in Genome Browser (JBrowse)
Model


Disease Annotations     Click to see Annotation Detail View

Gene Ontology Annotations     Click to see Annotation Detail View

Biological Process

Cellular Component

References
Additional References at PubMed
PMID:22301074   PMID:30032202  


Genomics

Comparative Map Data
Idh3a
(Ictidomys tridecemlineatus - thirteen-lined ground squirrel)
Squirrel AssemblyChrPosition (strand)SourceGenome Browsers
JBrowseNCBIUCSCEnsembl
HiC_Itri_2NW_024408640118,974,940 - 118,994,520 (-)NCBIHiC_Itri_2
SpeTri2.0 EnsemblNW_00493647136,822,971 - 36,842,610 (-)EnsemblSpeTri2.0SpeTri2.0 Ensembl
SpeTri2.0NW_00493647136,823,003 - 36,842,576 (-)NCBISpeTri2.0SpeTri2.0SpeTri2.0
IDH3A
(Homo sapiens - human)
Human AssemblyChrPosition (strand)SourceGenome Browsers
JBrowseNCBIUCSCEnsembl
GRCh381578,149,362 - 78,171,945 (+)NCBIGRCh38GRCh38hg38GRCh38
GRCh38.p14 Ensembl1578,131,498 - 78,171,945 (+)EnsemblGRCh38hg38GRCh38
GRCh371578,441,704 - 78,464,287 (+)NCBIGRCh37GRCh37hg19GRCh37
Build 361576,228,774 - 76,249,939 (+)NCBINCBI36Build 36hg18NCBI36
Build 341576,228,773 - 76,249,938NCBI
Celera1555,378,247 - 55,399,414 (+)NCBICelera
Cytogenetic Map15q25.1NCBI
HuRef1555,199,257 - 55,220,449 (+)NCBIHuRef
CHM1_11578,559,625 - 78,580,790 (+)NCBICHM1_1
T2T-CHM13v2.01576,011,920 - 76,034,530 (+)NCBIT2T-CHM13v2.0
Idh3a
(Mus musculus - house mouse)
Mouse AssemblyChrPosition (strand)SourceGenome Browsers
JBrowseNCBIUCSCEnsembl
GRCm39954,493,795 - 54,511,946 (+)NCBIGRCm39GRCm39mm39
GRCm39 Ensembl954,493,618 - 54,511,945 (+)EnsemblGRCm39 Ensembl
GRCm38954,586,511 - 54,604,662 (+)NCBIGRCm38GRCm38mm10GRCm38
GRCm38.p6 Ensembl954,586,334 - 54,604,661 (+)EnsemblGRCm38mm10GRCm38
MGSCv37954,434,318 - 54,452,469 (+)NCBIGRCm37MGSCv37mm9NCBIm37
MGSCv36954,384,648 - 54,402,799 (+)NCBIMGSCv36mm8
Celera951,829,728 - 51,847,959 (+)NCBICelera
Cytogenetic Map9A5.3NCBI
cM Map929.7NCBI
Idh3a
(Rattus norvegicus - Norway rat)
Rat AssemblyChrPosition (strand)SourceGenome Browsers
JBrowseNCBIUCSCEnsembl
GRCr8863,867,882 - 63,887,223 (+)NCBIGRCr8
mRatBN7.2854,971,694 - 54,991,085 (+)NCBImRatBN7.2mRatBN7.2
mRatBN7.2 Ensembl854,971,740 - 54,991,084 (+)EnsemblmRatBN7.2 Ensembl
UTH_Rnor_SHR_Utx860,505,281 - 60,524,691 (+)NCBIRnor_SHRUTH_Rnor_SHR_Utx
UTH_Rnor_SHRSP_BbbUtx_1.0858,784,271 - 58,803,675 (+)NCBIRnor_SHRSPUTH_Rnor_SHRSP_BbbUtx_1.0
UTH_Rnor_WKY_Bbb_1.0856,648,509 - 56,667,913 (+)NCBIRnor_WKYUTH_Rnor_WKY_Bbb_1.0
Rnor_6.0859,164,601 - 59,183,899 (+)NCBIRnor6.0Rnor_6.0rn6Rnor6.0
Rnor_6.0 Ensembl859,164,572 - 59,183,908 (+)EnsemblRnor6.0rn6Rnor6.0
Rnor_5.0857,745,463 - 57,764,761 (+)NCBIRnor5.0Rnor_5.0rn5Rnor5.0
RGSC_v3.4858,135,412 - 58,156,019 (+)NCBIRGSC3.4RGSC_v3.4rn4RGSC3.4
RGSC_v3.1858,154,465 - 58,175,073 (+)NCBI
Celera854,460,353 - 54,479,655 (+)NCBICelera
Cytogenetic Map8q24NCBI
Idh3a
(Chinchilla lanigera - long-tailed chinchilla)
Chinchilla AssemblyChrPosition (strand)SourceGenome Browsers
JBrowseNCBIUCSCEnsembl
ChiLan1.0 EnsemblNW_004955450685,905 - 703,586 (+)EnsemblChiLan1.0
ChiLan1.0NW_004955450685,905 - 703,593 (+)NCBIChiLan1.0ChiLan1.0
IDH3A
(Pan paniscus - bonobo/pygmy chimpanzee)
Bonobo AssemblyChrPosition (strand)SourceGenome Browsers
JBrowseNCBIUCSCEnsembl
NHGRI_mPanPan1-v21667,362,996 - 67,384,370 (+)NCBINHGRI_mPanPan1-v2
NHGRI_mPanPan11571,528,667 - 71,550,063 (+)NCBINHGRI_mPanPan1
Mhudiblu_PPA_v01557,078,588 - 57,099,934 (+)NCBIMhudiblu_PPA_v0Mhudiblu_PPA_v0panPan3
PanPan1.11576,043,311 - 76,064,634 (+)NCBIpanpan1.1PanPan1.1panPan2
PanPan1.1 Ensembl1576,043,311 - 76,064,634 (+)Ensemblpanpan1.1panPan2
IDH3A
(Canis lupus familiaris - dog)
Dog AssemblyChrPosition (strand)SourceGenome Browsers
JBrowseNCBIUCSCEnsembl
CanFam3.1358,301,982 - 58,318,925 (+)NCBICanFam3.1CanFam3.1canFam3CanFam3.1
CanFam3.1 Ensembl358,302,001 - 58,318,248 (+)EnsemblCanFam3.1canFam3CanFam3.1
Dog10K_Boxer_Tasha360,993,181 - 61,010,332 (+)NCBIDog10K_Boxer_Tasha
ROS_Cfam_1.0358,769,639 - 58,786,830 (+)NCBIROS_Cfam_1.0
ROS_Cfam_1.0 Ensembl358,748,159 - 58,786,830 (+)EnsemblROS_Cfam_1.0 Ensembl
UMICH_Zoey_3.1358,266,135 - 58,283,304 (+)NCBIUMICH_Zoey_3.1
UNSW_CanFamBas_1.0358,474,154 - 58,491,092 (+)NCBIUNSW_CanFamBas_1.0
UU_Cfam_GSD_1.0358,823,194 - 58,840,363 (+)NCBIUU_Cfam_GSD_1.0
IDH3A
(Sus scrofa - pig)
Pig AssemblyChrPosition (strand)SourceGenome Browsers
JBrowseNCBIUCSCEnsembl
Sscrofa11.1 Ensembl747,759,439 - 47,778,956 (-)EnsemblSscrofa11.1susScr11Sscrofa11.1
Sscrofa11.1747,759,436 - 47,778,948 (-)NCBISscrofa11.1Sscrofa11.1susScr11Sscrofa11.1
Sscrofa10.2753,312,283 - 53,330,719 (-)NCBISscrofa10.2Sscrofa10.2susScr3
IDH3A
(Chlorocebus sabaeus - green monkey)
Green Monkey AssemblyChrPosition (strand)SourceGenome Browsers
JBrowseNCBIUCSCEnsembl
ChlSab1.1265,183,470 - 5,205,385 (-)NCBIChlSab1.1ChlSab1.1chlSab2
ChlSab1.1 Ensembl265,184,991 - 5,205,384 (-)EnsemblChlSab1.1ChlSab1.1 EnsemblchlSab2
Vero_WHO_p1.0NW_023666048136,598,251 - 136,620,304 (+)NCBIVero_WHO_p1.0Vero_WHO_p1.0
Idh3a
(Heterocephalus glaber - naked mole-rat)
Naked Mole-Rat AssemblyChrPosition (strand)SourceGenome Browsers
JBrowseNCBIUCSCEnsembl
HetGla_female_1.0 EnsemblNW_0046248942,662,434 - 2,679,232 (-)EnsemblHetGla_female_1.0HetGla_female_1.0 EnsemblhetGla2
HetGla 1.0NW_0046248942,661,509 - 2,679,071 (-)NCBIHetGla_female_1.0HetGla 1.0hetGla2


Expression

RNA-SEQ Expression


Sequence


Ensembl Acc Id: ENSSTOT00000026679   ⟹   ENSSTOP00000022121
Type: CODING
Position:
Squirrel AssemblyChrPosition (strand)Source
SpeTri2.0 EnsemblNW_00493647136,824,424 - 36,838,027 (-)Ensembl
Ensembl Acc Id: ENSSTOT00000038148   ⟹   ENSSTOP00000027794
Type: CODING
Position:
Squirrel AssemblyChrPosition (strand)Source
SpeTri2.0 EnsemblNW_00493647136,822,971 - 36,842,610 (-)Ensembl
RefSeq Acc Id: XM_005316859   ⟹   XP_005316916
Type: CODING
Position:
Squirrel AssemblyChrPosition (strand)Source
HiC_Itri_2NW_024408640118,974,940 - 118,994,520 (-)NCBI
SpeTri2.0NW_00493647136,823,003 - 36,842,576 (-)NCBI
Sequence:
RefSeq Acc Id: XM_040276298   ⟹   XP_040132232
Type: CODING
Position:
Squirrel AssemblyChrPosition (strand)Source
HiC_Itri_2NW_024408640118,974,940 - 118,994,520 (-)NCBI
Protein Sequences
Protein RefSeqs XP_005316916 (Get FASTA)   NCBI Sequence Viewer  
  XP_040132232 (Get FASTA)   NCBI Sequence Viewer  
Ensembl Protein ENSSTOP00000022121.2
  ENSSTOP00000027794.1
GenBank Protein KAG3262387 (Get FASTA)   NCBI Sequence Viewer  
RefSeq Acc Id: XP_005316916   ⟸   XM_005316859
- Peptide Label: isoform X1
- UniProtKB: I3NCM4 (UniProtKB/TrEMBL),   A0A287D2N7 (UniProtKB/TrEMBL)
- Sequence:
RefSeq Acc Id: XP_040132232   ⟸   XM_040276298
- Peptide Label: isoform X2
- UniProtKB: I3NCM4 (UniProtKB/TrEMBL)
Ensembl Acc Id: ENSSTOP00000022121   ⟸   ENSSTOT00000026679
Ensembl Acc Id: ENSSTOP00000027794   ⟸   ENSSTOT00000038148

Additional Information

Database Acc Id Source(s)
Ensembl Genes ENSSTOG00000022510 Ensembl, UniProtKB/TrEMBL
Ensembl Transcript ENSSTOT00000026679.2 UniProtKB/TrEMBL
  ENSSTOT00000038148.1 UniProtKB/TrEMBL
Gene3D-CATH Isopropylmalate Dehydrogenase UniProtKB/TrEMBL
InterPro IsoCit/isopropylmalate_DH_CS UniProtKB/TrEMBL
  Isocitrate_DH_NAD UniProtKB/TrEMBL
  IsoPropMal-DH-like_dom UniProtKB/TrEMBL
NCBI Gene Idh3a ENTREZGENE
PANTHER DECARBOXYLATING DEHYDROGENASES-ISOCITRATE, ISOPROPYLMALATE, TARTRATE UniProtKB/TrEMBL
  ISOCITRATE DEHYDROGENASE [NAD] SUBUNIT ALPHA, MITOCHONDRIAL UniProtKB/TrEMBL
Pfam Iso_dh UniProtKB/TrEMBL
PROSITE IDH_IMDH UniProtKB/TrEMBL
SMART Iso_dh UniProtKB/TrEMBL
Superfamily-SCOP Isocitrate/Isopropylmalate dehydrogenase-like UniProtKB/TrEMBL
UniProt A0A287D2N7 ENTREZGENE, UniProtKB/TrEMBL
  I3NCM4 ENTREZGENE, UniProtKB/TrEMBL


Nomenclature History
Date Current Symbol Current Name Previous Symbol Previous Name Description Reference Status
2019-07-16 Idh3a  isocitrate dehydrogenase (NAD(+)) 3 catalytic subunit alpha  Idh3a  isocitrate dehydrogenase (NAD(+)) 3 alpha  Symbol and/or name change 5135510 APPROVED
2019-04-16 Idh3a  isocitrate dehydrogenase (NAD(+)) 3 alpha    isocitrate dehydrogenase 3 (NAD(+)) alpha  Symbol and/or name change 5135510 APPROVED