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Ontology Browser

Term:
Parent Terms Term With Siblings Child Terms
benign soft tissue neoplasm +   
central nervous system mesenchymal non-meningothelial tumor +  
congenital epulis 
Desmoid-type fibromatosis +  
fibromyxoid tumor +  
glomus tumor +  
inflammatory myofibroblastic tumor +  
A multinodular intermediate fibroblastic neoplasm that arises from soft tissue or viscera, in children and young adults. It is characterized by the presence of spindle-shaped fibroblasts and myofibroblasts, and a chronic inflammatory infiltrate composed of eosinophils, lymphocytes, and plasma cells.
juvenile hyaline fibromatosis 
kaposiform hemangioendothelioma 
malignant soft tissue neoplasm +  
Mazabraud syndrome 
mediastinal mesenchymal tumor +  
mixed endometrial stromal and smooth muscle tumor +  
nodular fasciitis 
PEComa +   
soft tissue amyloid neoplasm 
synovium neoplasm +  

Synonyms
Exact Synonyms: DOID:0050905 ;   IMT ;   NCIT:C6481 ;   Orphanet:178342 ;   http://identifiers.org/medgen/137723 ;   http://identifiers.org/mesh/D006104 ;   http://linkedlifedata.com/resource/umls/id/C0334121 ;   inflammatory fibrosarcoma ;   inflammatory myofibroblastic neoplasm ;   inflammatory pseudotumor
Synonyms: http://identifiers.org/meddra/10067917
Alternate IDs: MONDO:0015798
Xrefs: DOID:0050905 ;   GARD:7146 ;   ICDO:8825/1 ;   MEDGEN:137723 ;   MESH:D006104 ;   MedDRA:10067917 ;   NCI:C6481 ;   ONCOTREE:IMT ;   ORDO:178342 ;   UMLS:C0334121
see_also: https://rarediseases.info.nih.gov/diseases/7146/inflammatory-myofibroblastic-tumor" xsd:anyURI {source="GARD:0007146
Definition Sources: NCIT:P378

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