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Ontology Browser

Term:
Parent Terms Term With Siblings Child Terms
atypical progressive supranuclear palsy syndrome +  
supranuclear palsy, progressive, 1 
Classical progressive supranuclear palsy, also known as Richardson's syndrome, is the most common clinical variant of progressive supranuclear palsy (PSP), a rare late-onset neurodegenerative disease characterized by postural instability, progressive rigidity, supranuclear gaze palsy and mild dementia.

Synonyms
Exact Synonyms: PSP ;   Richardson syndrome ;   Steele-Richardson-Olszewski disease ;   Steele-Richardson-Olszewski syndrome ;   classic PSP syndrome ;   classic progressive supranuclear palsy syndrome ;   supranuclear palsy, progressive ;   supranuclear palsy, progressive, type 1
Related Synonyms: PSNP1
Alternate IDs: MONDO:0010997
Xrefs: GARD:17182 ;   MEDGEN:1640811 ;   MIM:601104 ;   ORDO:240071 ;   UMLS:C4551863
Definition Sources: Orphanet:240071

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