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Ontology Browser
Term:
Parent Terms Term With Siblings Child Terms
Alagille syndrome +  
Bile acid synthesis defect with cholestasis and malabsorption +  
bile duct disorder +   
bile duct neoplasm +   
bile reflux 
biliary tract cancer +   
biliary tract neoplasm +   
cholestasis, intrahepatic, of pregnancy 3 
dicrocoeliasis 
Ductal or Ductular Proliferation 
gallbladder disease +   
gallbladder neoplasm +   
Intrahepatic cholestasis of pregnancy  
isolated agenesis of gallbladder 
postcholecystectomy syndrome 
primary biliary cirrhosis  
An autoimmune inflammatory disorder characterized by destruction of the small intrahepatic bile ducts. It affects predominantly females and it may lead to cirrhosis and liver failure. Patients have antimitochondrial and antinuclear antibodies in the peripheral blood. Primary biliary cholangitis (PBC) is a chronic and slowly progressive cholestatic liver disease of autoimmune etiology characterized by injury of the intrahepatic bile ducts that may eventually lead to liver failure.
secondary biliary cirrhosis 

Synonyms
Exact Synonyms: Hanot syndrome ;   PBC ;   biliary liver cirrhosis ;   cholestatic cirrhosis ;   chronic non-suppurative destructive cholangitis ;   chronic nonsuppurative destructive cholangitis ;   primary Bilary cirrhosis (PBC) ;   primary biliary cholangitis
Related Synonyms: familial primary biliary cirrhosis
Xrefs: DOID:12236 ;   GARD:7459 ;   HP:0002613 ;   ICD10:K74.3 ;   ICD9:571.6 ;   MEDGEN:3035 ;   MESH:D008105 ;   MIM:PS109720 ;   MONDO:0005388 ;   MP:0003256
Definition Sources: Orphanet:186

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