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Ontology Browser

Term:
Parent Terms Term With Siblings Child Terms
breast fibrosis 
Chronic Eosinophilic Leukemia, Not Otherwise Specified 
chronic myelogenous leukemia +   
Chronic Neutrophilic Leukemia 
cirrhosis of liver +   
endomyocardial fibrosis 
erythroid neoplasm +   
essential thrombocythemia 
idiopathic aplastic anemia +   
inherited aplastic anemia +  
Myelodysplastic/Myeloproliferative Neoplasm +  
myelofibrosis 
myeloid leukemia +   
myeloproliferative neoplasm, unclassifiable 
paroxysmal nocturnal hemoglobinuria +  
Peritoneal Fibrosis 
polycythemia vera  
primary acquired red cell aplasia +  
primary myelofibrosis +  
Myelofibrosis with myeloid metaplasia is a myeloproliferative disease with annual incidence of approximately 1 case per 100,000 individuals and age at diagnosis around 60 (an increased prevalence is noted in Ashkenazi Jews). Clinical manifestations depend on the type of blood cell affected and may include anemia, pallor, splenomegaly, hypermetabolic state, petechiae, ecchymosis, bleeding, lymphadenopathy, hepatomegaly, portal hypertension.
pulmonary fibrosis +   
Rare constitutional medullar aplasia +  
renal fibrosis 
Therapy-Related Myeloid Neoplasm 
transient myeloproliferative syndrome 

Synonyms
Exact Synonyms: AMM ;   Agnogenic myeloid metaplasia ;   CIMF ;   DOID:4971 ;   NCIT:C2862 ;   Orphanet:824 ;   aleukemic myelosis ;   bone marrow fibrosis ;   chronic idiopathic myelofibrosis ;   http://identifiers.org/medgen/7929
Synonyms: http://identifiers.org/snomedct/128843003 ;   http://identifiers.org/snomedct/154841009 ;   http://identifiers.org/snomedct/188773009 ;   http://identifiers.org/snomedct/22265001 ;   http://identifiers.org/snomedct/267572005 ;   http://identifiers.org/snomedct/307651005 ;   http://identifiers.org/snomedct/52967002 ;   http://identifiers.org/snomedct/78956007 ;   http://linkedlifedata.com/resource/umls/id/C0026987
Narrow Synonyms: myelofibrosis with myeloid metaplasia
Related Synonyms: myelofibrosis ;   myeloid metaplasia
Xrefs: COHD:133169 ;   DOID:4971 ;   GARD:8618 ;   ICD10:D47.4 ;   ICD10:D75.81 ;   ICD9:238.76 ;   ICD9:289.83 ;   ICDO:9961/3 ;   MEDGEN:7929 ;   MESH:D055728
Definition Sources: Orphanet:824

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