A malignant epithelial neoplasm of the kidney characterized by the presence of lipid-containing clear cells within a vascular network. The tumor may metastasize to unusual sites and late metastasis is common.
Endometrial Clear Cell Adenocarcinoma
extrahepatic bile duct clear cell adenocarcinoma +
fallopian tube clear cell adenocarcinoma
hepatocellular clear cell carcinoma
hereditary renal cell carcinoma +
Hidradenocarcinoma
ovarian clear cell adenocarcinoma +
papillary renal cell carcinoma +
Renal Cell Carcinoma Associated with Xp11.2 Translocations/TFE3 Gene Fusions