MAMMALIAN PHENOTYPE - ANNOTATIONS
The Mouse Adult Gross Anatomy Ontology and Mammalian Phenotype Ontology are downloaded weekly from the Mouse Genome Informatics databases at Jackson Laboratories (ftp://ftp.informatics.jax.org/pub/reports/index.html). For more information about these ontologies, see the MGI Publications Page at http://www.informatics.jax.org/mgihome/other/publications.shtml.
Term: abnormal mitochondrial physiology
Accession: MP:0006036
browse the term
Definition: any functional anomaly of the cellular organelles responsible for energy production
Synonyms: narrow_synonym: Abnormality of mitochondrial metabolism
xref: HP:0003287
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2500002B13Rik
RIKEN cDNA 2500002B13 gene
IAGP
MGI
PMID:33953175
NCBI chr 8:57,940,997...57,963,296
Ensembl chr 8:57,940,551...57,964,030
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A1cf
APOBEC1 complementation factor
IAGP
MGI
PMID:20644257 PMID:26356605 PMID:27184846 PMID:31209364 PMID:35680100
NCBI chr19:31,846,156...31,929,765
Ensembl chr19:31,846,164...31,926,395
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AA467197
expressed sequence AA467197
IAGP
MGI
PMID:38296961
NCBI chr 2:122,479,807...122,482,996
Ensembl chr 2:122,478,906...122,483,111
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Abcb10
ATP-binding cassette, sub-family B member 10
IAGP
MGI
PMID:21788586
NCBI chr 8:124,679,198...124,709,877
Ensembl chr 8:124,679,198...124,709,861
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Abcb6
ATP-binding cassette, sub-family B member 6
IAGP
MGI
PMID:22294697
NCBI chr 1:75,148,284...75,157,066
Ensembl chr 1:75,148,361...75,157,036
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Abcc9
ATP-binding cassette, sub-family C member 9
IAGP
MGI
PMID:24648545
NCBI chr 6:142,533,592...142,648,472
Ensembl chr 6:142,533,588...142,648,041
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Abcg2
ATP binding cassette subfamily G member 2 (Junior blood group)
IAGP
MGI
PMID:23954234
NCBI chr 6:58,561,476...58,669,436
Ensembl chr 6:58,561,508...58,672,661
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Acad9
acyl-Coenzyme A dehydrogenase family, member 9
IAGP
MGI
PMID:34556413
NCBI chr 3:36,120,128...36,147,006
Ensembl chr 3:36,120,128...36,147,002
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Adck2
aarF domain containing kinase 2
IAGP
MGI
PMID:31480808
NCBI chr 6:39,550,778...39,565,703
Ensembl chr 6:39,550,807...39,565,703
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Afg3l1
AFG3-like AAA ATPase 1
IAGP
MGI
PMID:27911893
NCBI chr 8:124,204,601...124,230,655
Ensembl chr 8:124,204,642...124,230,655
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Afg3l2
AFG3-like AAA ATPase 2
IAGP
MGI
PMID:27911893
NCBI chr18:67,537,830...67,582,277
Ensembl chr18:67,537,834...67,582,242
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Aifm1
apoptosis-inducing factor, mitochondrion-associated 1
IAGP
MGI
PMID:16287843 PMID:16917506
NCBI chr X:47,563,821...47,602,440
Ensembl chr X:47,563,821...47,602,440
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Alkbh7
alkB homolog 7
IAGP
MGI
PMID:23572141
NCBI chr17:57,304,339...57,306,340
Ensembl chr17:57,304,339...57,306,322
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Alpl
alkaline phosphatase, liver/bone/kidney
IAGP
MGI
PMID:30998386
NCBI chr 4:137,469,042...137,523,695
Ensembl chr 4:137,469,044...137,523,695
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Altre
aging liver Treg-expressed non-protein coding RNA
IAGP
MGI
PMID:37277640
NCBI chr 7:67,916,087...67,926,342
Ensembl chr 7:67,915,783...67,930,487
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Ano5
anoctamin 5
IAGP
MGI
PMID:26911675
NCBI chr 7:51,160,668...51,248,459
Ensembl chr 7:51,160,777...51,248,457
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Apaf1
apoptotic peptidase activating factor 1
IAGP
MGI
PMID:16917506
NCBI chr10:90,825,173...90,918,688
Ensembl chr10:90,825,173...90,918,632
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Atp7a
ATPase, copper transporting, alpha polypeptide
IAGP
MGI
PMID:9342151
NCBI chr X:105,070,830...105,171,766
Ensembl chr X:105,070,882...105,168,532
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Atpaf1
ATP synthase mitochondrial F1 complex assembly factor 1
IAGP
MGI
PMID:34375736
NCBI chr 4:115,642,025...115,669,120
Ensembl chr 4:115,642,009...115,679,852
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Bcs1l
BCS1 homolog, ubiquinol-cytochrome c reductase complex chaperone
IAGP
MGI
PMID:21274865 PMID:28424480
NCBI chr 1:74,627,448...74,631,602
Ensembl chr 1:74,627,448...74,631,602
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Bid
BH3 interacting domain death agonist
IAGP
MGI
PMID:10476969
NCBI chr 6:120,870,080...120,894,074
Ensembl chr 6:120,868,891...120,893,814
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Bloc1s1
biogenesis of lysosomal organelles complex-1, subunit 1
IAGP
MGI
PMID:24356961
NCBI chr10:128,755,783...128,759,393
Ensembl chr10:128,753,751...128,759,904
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Bola3
bolA family member 3
IAGP
MGI
PMID:32313871
NCBI chr 6:83,326,129...83,337,118
Ensembl chr 6:83,326,129...83,337,118
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Cacna1s
calcium channel, voltage-dependent, L type, alpha 1S subunit
IAGP
MGI
PMID:26965373
NCBI chr 1:135,980,549...136,047,268
Ensembl chr 1:135,980,488...136,047,560
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Cars2
cysteinyl-tRNA synthetase 2, mitochondrial
IAGP
MGI
PMID:29079736
NCBI chr 8:11,564,017...11,600,781
Ensembl chr 8:11,563,977...11,600,783
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Ccdc51
coiled-coil domain containing 51
IAGP
MGI
PMID:31435016
NCBI chr 9:108,911,564...108,922,431
Ensembl chr 9:108,911,561...108,921,557
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Cd19
CD19 antigen
IAGP
MGI
PMID:32609329
NCBI chr 7:126,007,620...126,016,401
Ensembl chr 7:126,007,622...126,014,061
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Cd47
CD47 antigen (Rh-related antigen, integrin-associated signal transducer)
IAGP
MGI
PMID:17293482
NCBI chr16:49,671,691...49,732,799
Ensembl chr16:49,620,896...49,735,373
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Cdk5rap1
CDK5 regulatory subunit associated protein 1
IAGP
MGI
PMID:25738458
NCBI chr 2:154,063,931...154,216,170
Ensembl chr 2:154,177,300...154,214,930
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Cert1
ceramide transporter 1
IAGP
MGI
PMID:19139267
NCBI chr13:96,679,243...96,782,362
Ensembl chr13:96,679,243...96,776,675
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Chchd10
coiled-coil-helix-coiled-coil-helix domain containing 10
IAGP
MGI
PMID:35700042
NCBI chr10:75,768,964...75,773,584
Ensembl chr10:75,768,964...75,773,581
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Coasy
Coenzyme A synthase
IAGP
MGI
PMID:33352696
NCBI chr11:100,973,391...100,977,445
Ensembl chr11:100,973,391...100,977,445
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Coq6
coenzyme Q6 monooxygenase
IAGP
MGI
PMID:30737270
NCBI chr12:84,408,530...84,420,570
Ensembl chr12:84,408,431...84,420,570
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Coq7
demethyl-Q 7
IAGP
MGI
PMID:23045551
NCBI chr 7:118,108,881...118,132,529
Ensembl chr 7:118,108,882...118,132,579
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Coq9
coenzyme Q9
IAGP
MGI
PMID:23255162
NCBI chr 8:95,565,041...95,581,523
Ensembl chr 8:95,564,949...95,581,523
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Cox10
heme A:farnesyltransferase cytochrome c oxidase assembly factor 10
IAGP
MGI
PMID:22914734
NCBI chr11:63,853,453...63,970,298
Ensembl chr11:63,853,453...63,970,294
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Dnajc30
DnaJ heat shock protein family (Hsp40) member C30
IAGP
MGI
PMID:30318146
NCBI chr 5:135,093,060...135,094,219
Ensembl chr 5:135,093,056...135,094,716
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Egln2
egl-9 family hypoxia-inducible factor 2
IAGP
MGI
PMID:18176562
NCBI chr 7:26,858,083...26,866,227
Ensembl chr 7:26,858,083...26,866,227
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Eif4ebp1
eukaryotic translation initiation factor 4E binding protein 1
IAGP
MGI
PMID:20644257
NCBI chr 8:27,750,355...27,765,684
Ensembl chr 8:27,750,357...27,766,702
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Elac2
elaC ribonuclease Z 2
IAGP
MGI
PMID:30126926
NCBI chr11:64,869,856...64,892,906
Ensembl chr11:64,869,864...64,892,895
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Etfbkmt
electron transfer flavoprotein beta subunit lysine methyltransferase
IAGP
MGI
PMID:29352221
NCBI chr 6:149,042,980...149,052,669
Ensembl chr 6:149,041,347...149,052,669
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Fars2
phenylalanine-tRNA synthetase 2, mitochondrial
IAGP
MGI
PMID:35794642
NCBI chr13:36,301,373...36,721,569
Ensembl chr13:36,301,395...36,910,254
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Fbxl5
F-box and leucine-rich repeat protein 5
IAGP
MGI
PMID:21907140
NCBI chr 5:43,901,958...43,939,529
Ensembl chr 5:43,901,957...43,978,980
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Fis1
fission, mitochondrial 1
IAGP
MGI
PMID:31526891
NCBI chr 5:136,982,129...136,995,088
Ensembl chr 5:136,982,129...136,995,088
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Fnip1
folliculin interacting protein 1
IAGP
MGI
PMID:25775561
NCBI chr11:54,328,071...54,409,067
Ensembl chr11:54,329,025...54,409,061
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Fnip2
folliculin interacting protein 2
IAGP
MGI
PMID:25775561
NCBI chr 3:79,363,556...79,475,458
Ensembl chr 3:79,363,281...79,475,103
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Foxg1
forkhead box G1
IAGP
MGI
PMID:16917506
NCBI chr12:49,429,666...49,433,650
Ensembl chr12:49,429,443...49,433,644
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Foxo1
forkhead box O1
IAGP
MGI
PMID:25264246
NCBI chr 3:52,175,758...52,257,530
Ensembl chr 3:52,175,757...52,260,642
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Foxo3
forkhead box O3
IAGP
MGI
PMID:25264246
NCBI chr10:42,057,841...42,152,691
Ensembl chr10:42,057,837...42,152,751
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Foxo4
forkhead box O4
IAGP
MGI
PMID:25264246
NCBI chr X:100,297,855...100,304,479
Ensembl chr X:100,298,134...100,304,479
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Foxp3
forkhead box P3
IAGP
MGI
PMID:37277640
NCBI chr X:7,445,915...7,461,482
Ensembl chr X:7,439,883...7,461,484
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Fth1
ferritin heavy polypeptide 1
IAGP
MGI
PMID:19492434
NCBI chr19:9,957,964...9,962,475
Ensembl chr19:9,957,962...9,962,462
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Fxn
frataxin
IAGP
MGI
PMID:32586831
NCBI chr19:24,236,909...24,257,954
Ensembl chr19:24,238,817...24,257,969
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Gadd45gip1
growth arrest and DNA-damage-inducible, gamma interacting protein 1
IAGP
MGI
PMID:25660120
NCBI chr 8:85,558,911...85,562,111
Ensembl chr 8:85,558,151...85,562,111
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Gclc
glutamate-cysteine ligase, catalytic subunit
IAGP
MGI
PMID:17464988
NCBI chr 9:77,661,817...77,701,771
Ensembl chr 9:77,661,817...77,701,767
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Gfer
growth factor, augmenter of liver regeneration
IAGP
MGI
PMID:25977511
NCBI chr17:24,912,164...24,915,065
Ensembl chr17:24,912,161...24,915,503
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Gpx1
glutathione peroxidase 1
IAGP
MGI
PMID:10754271
NCBI chr 9:108,216,279...108,217,541
Ensembl chr 9:108,216,102...108,217,542
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Gpx4
glutathione peroxidase 4
IAGP
MGI
PMID:18206984 PMID:19783653
NCBI chr10:79,883,000...79,892,273
Ensembl chr10:79,883,000...79,892,273
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Gt(ROSA)26Sor
gene trap ROSA 26, Philippe Soriano
IAGP
MGI
PMID:21091282 PMID:21768369 PMID:26356605 PMID:27911893 PMID:35680100
NCBI chr 6:113,044,389...113,054,205
Ensembl chr 6:113,043,843...113,055,336
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Hacd2
3-hydroxyacyl-CoA dehydratase 2
IAGP
MGI
PMID:36693621
NCBI chr16:34,842,791...34,929,560
Ensembl chr16:34,842,798...34,929,547
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Hat1
histone aminotransferase 1
IAGP
MGI
PMID:31290578
NCBI chr 2:71,219,604...71,271,966
Ensembl chr 2:71,219,302...71,271,966
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Hint2
histidine triad nucleotide binding protein 2
IAGP
MGI
PMID:22961760
NCBI chr 4:43,654,227...43,656,445
Ensembl chr 4:43,654,227...43,656,466
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Hmox1
heme oxygenase 1
IAGP
MGI
PMID:24995976
NCBI chr 8:75,820,246...75,827,221
Ensembl chr 8:75,820,249...75,827,217
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Hoxa11os
homeobox A11, opposite strand
IAGP
MGI
PMID:37494932
NCBI chr 6:52,222,013...52,226,770
Ensembl chr 6:52,220,356...52,226,784
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Hprt1
hypoxanthine phosphoribosyltransferase 1
IAGP
MGI
PMID:24055366
NCBI chr X:52,076,955...52,110,537
Ensembl chr X:52,077,014...52,110,536
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Hspb2
heat shock protein 2
IAGP
MGI
PMID:22870288
NCBI chr 9:50,662,372...50,663,654
Ensembl chr 9:50,662,378...50,663,654
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Hspd1
heat shock protein 1 (chaperonin)
IAGP
MGI
PMID:31209364
NCBI chr 1:55,116,992...55,127,402
Ensembl chr 1:55,116,994...55,127,402
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Immt
inner membrane protein, mitochondrial
IAGP
MGI
PMID:36974636
NCBI chr 6:71,806,200...71,852,250
Ensembl chr 6:71,808,315...71,854,372
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Jund
jun D proto-oncogene
IAGP
MGI
PMID:15655111
NCBI chr 8:71,150,389...71,153,265
Ensembl chr 8:71,151,599...71,153,265
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Lama2
laminin, alpha 2
IAGP
MGI
PMID:32017711
NCBI chr10:26,857,281...27,493,021
Ensembl chr10:26,856,032...27,495,754
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Lancl1
LanC (bacterial lantibiotic synthetase component C)-like 1
IAGP
MGI
PMID:25158856
NCBI chr 1:67,039,676...67,078,049
Ensembl chr 1:67,039,676...67,078,031
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Ldlr
low density lipoprotein receptor
IAGP
MGI
PMID:38123514
NCBI chr 9:21,634,872...21,661,215
Ensembl chr 9:21,634,779...21,661,215
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Lepr
leptin receptor
IAGP
MGI
PMID:22326220
NCBI chr 4:101,574,393...101,676,375
Ensembl chr 4:101,574,601...101,672,549
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Letm1
leucine zipper-EF-hand containing transmembrane protein 1
IAGP
MGI
PMID:23716663
NCBI chr 5:33,897,017...33,940,061
Ensembl chr 5:33,897,017...33,940,161
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Lrpprc
leucine-rich PPR-motif containing
IAGP
MGI
PMID:22045337
NCBI chr17:85,012,675...85,098,214
Ensembl chr17:85,012,675...85,098,217
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Lyz2
lysozyme 2
IAGP
MGI
PMID:24995976
NCBI chr10:117,113,446...117,118,177
Ensembl chr10:117,113,236...117,118,226
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Mcat
malonyl CoA:ACP acyltransferase (mitochondrial)
IAGP
MGI
PMID:23077570
NCBI chr15:83,430,998...83,439,936
Ensembl chr15:83,430,998...83,447,988
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Mcu
mitochondrial calcium uniporter
IAGP
MGI
PMID:24212091 PMID:27184846 PMID:31501572
NCBI chr10:59,282,806...59,453,231
Ensembl chr10:59,282,806...59,452,514
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Mcur1
mitochondrial calcium uniporter regulator 1
IAGP
MGI
PMID:27184846
NCBI chr13:43,691,882...43,714,284
Ensembl chr13:43,691,869...43,713,667
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Mecr
mitochondrial trans-2-enoyl-CoA reductase
IAGP
MGI
PMID:28369354
NCBI chr 4:131,570,755...131,595,097
Ensembl chr 4:131,570,781...131,595,097
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Med30
mediator complex subunit 30
IEA
MGI
NCBI chr15:52,575,841...52,593,827
Ensembl chr15:52,575,804...52,593,960
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Mettl1
methyltransferase 1, tRNA methylguanosine
IAGP
MGI
PMID:39255038
NCBI chr10:126,877,287...126,882,234
Ensembl chr10:126,877,283...126,882,234
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Mfn1
mitofusin 1
IAGP
MGI
PMID:12527753
NCBI chr 3:32,583,594...32,633,384
Ensembl chr 3:32,583,614...32,633,388
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Mfn2
mitofusin 2
IAGP
MGI
PMID:12527753 PMID:20335458
NCBI chr 4:147,958,043...147,989,527
Ensembl chr 4:147,958,056...147,989,161
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Mgme1
mitochondrial genome maintenance exonuclease 1
IAGP
MGI
PMID:29572490
NCBI chr 2:144,112,824...144,123,147
Ensembl chr 2:144,112,583...144,123,147
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Micu1
mitochondrial calcium uptake 1
IAGP
MGI
PMID:27477272
NCBI chr10:59,538,385...59,699,956
Ensembl chr10:59,538,299...59,699,954
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Micu2
mitochondrial calcium uptake 2
IAGP
MGI
PMID:29073106
NCBI chr14:58,153,718...58,236,716
Ensembl chr14:58,153,718...58,236,719
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Mir378a
microRNA 378a
IAGP
MGI
PMID:22949648
NCBI chr18:61,530,906...61,530,971
Ensembl chr18:61,530,906...61,530,971
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Mpc1
mitochondrial pyruvate carrier 1
IAGP
MGI
PMID:26344103
NCBI chr17:8,502,590...8,516,499
Ensembl chr17:8,501,736...8,516,493
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Mpc2
mitochondrial pyruvate carrier 2
IAGP
MGI
PMID:24910426
NCBI chr 1:165,288,829...165,308,787
Ensembl chr 1:165,288,206...165,308,783
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Mrpl22
mitochondrial ribosomal protein L22
IAGP
MGI
PMID:32376682
NCBI chr11:58,060,850...58,070,406
Ensembl chr11:58,062,487...58,070,391
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Mrpl3
mitochondrial ribosomal protein L3
IAGP
MGI
PMID:32376682
NCBI chr 9:104,930,394...104,954,665
Ensembl chr 9:104,930,438...104,957,087
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Mrpl44
mitochondrial ribosomal protein L44
IAGP
MGI
PMID:32376682
NCBI chr 1:79,753,735...79,759,162
Ensembl chr 1:79,753,735...79,759,162
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Mrps12
mitochondrial ribosomal protein S12
IAGP
MGI
PMID:31721250
NCBI chr 7:28,439,066...28,441,246
Ensembl chr 7:28,439,066...28,441,245
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Mrps18c
mitochondrial ribosomal protein S18C
IAGP
MGI
PMID:32376682
NCBI chr 5:100,946,625...100,952,333
Ensembl chr 5:100,946,493...100,952,337
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Mrps22
mitochondrial ribosomal protein S22
IAGP
MGI
PMID:32376682
NCBI chr 9:98,470,783...98,483,732
Ensembl chr 9:98,470,783...98,483,713
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Mrs2
MRS2 magnesium transporter
IAGP
MGI
PMID:33035451
NCBI chr13:25,171,466...25,204,345
Ensembl chr13:25,171,466...25,204,362
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Mss51
MSS51 mitochondrial translational activator
IAGP
MGI
PMID:29913553
NCBI chr14:20,532,925...20,546,969
Ensembl chr14:20,532,935...20,546,969
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mt-Nd6
NADH dehydrogenase 6, mitochondrial
IAGP
MGI
PMID:23129651 PMID:27626666
NCBI chr MT:13,552...14,070
Ensembl chr MT:13,552...14,070
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mt-Ta
tRNA alanine, mitochondrial
IAGP
MGI
PMID:27626666
NCBI chr MT:5,018...5,086
Ensembl chr MT:5,018...5,086
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mt-Tl1
tRNA leucine 1, mitochondrial
IAGP
MGI
PMID:35998911
NCBI chr MT:2,676...2,750
Ensembl chr MT:2,676...2,750
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Mterf3
mitochondrial transcription termination factor 3
IAGP
MGI
PMID:17662942
NCBI chr13:67,053,520...67,081,148
Ensembl chr13:67,055,032...67,081,152
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Mterf4
mitochondrial transcription termination factor 4
IAGP
MGI
PMID:21531335
NCBI chr 1:93,228,927...93,233,601
Ensembl chr 1:93,226,933...93,233,637
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Mtfmt
mitochondrial methionyl-tRNA formyltransferase
IAGP
MGI
PMID:36983072
NCBI chr 9:65,343,064...65,360,336
Ensembl chr 9:65,343,064...65,360,336
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Mtfp1
mitochondrial fission process 1
IAGP
MGI
PMID:36333300
NCBI chr11:4,041,481...4,045,431
Ensembl chr11:4,041,480...4,045,445
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Mtm1
X-linked myotubular myopathy gene 1
IAGP
MGI
PMID:23109424
NCBI chr X:70,254,373...70,359,019
Ensembl chr X:70,254,373...70,359,297
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Mto1
mitochondrial tRNA translation optimization 1
IAGP
MGI
PMID:25506927
NCBI chr 9:78,355,372...78,381,447
Ensembl chr 9:78,355,490...78,382,630
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Mtor
mechanistic target of rapamycin kinase
IAGP
MGI
PMID:20644257
NCBI chr 4:148,533,039...148,642,142
Ensembl chr 4:148,533,068...148,642,140
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Myl2
myosin, light polypeptide 2, regulatory, cardiac, slow
IAGP
MGI
PMID:40461459
NCBI chr 5:122,230,787...122,251,536
Ensembl chr 5:122,239,014...122,251,535
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Ndor1
NADPH dependent diflavin oxidoreductase 1
IAGP
MGI
PMID:24589777
NCBI chr 2:25,134,825...25,145,458
Ensembl chr 2:25,134,833...25,146,034 Ensembl chr 2:25,134,833...25,146,034 Ensembl chr 2:25,134,833...25,146,034
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Ndufa13
NADH:ubiquinone oxidoreductase subunit A13
IAGP
MGI
PMID:35312628
NCBI chr 8:70,346,813...70,355,208
Ensembl chr 8:70,346,830...70,355,208
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Noa1
nitric oxide associated 1
IAGP
MGI
PMID:21118999
NCBI chr 5:77,442,016...77,458,276
Ensembl chr 5:77,442,029...77,457,931
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Nos1
nitric oxide synthase 1, neuronal
IAGP
MGI
PMID:16246868
NCBI chr 5:118,004,904...118,096,905
Ensembl chr 5:117,919,097...118,096,905
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Nox4
NADPH oxidase 4
IAGP
MGI
PMID:20713697
NCBI chr 7:86,893,638...87,047,918
Ensembl chr 7:86,895,304...87,047,918
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Npc1
NPC intracellular cholesterol transporter 1
IAGP
MGI
PMID:15644330
NCBI chr18:12,322,751...12,369,851
Ensembl chr18:12,322,749...12,369,457
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Nrf1
nuclear respiratory factor 1
IAGP
MGI
PMID:30333037
NCBI chr 6:30,047,984...30,153,462
Ensembl chr 6:30,047,987...30,153,457
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Nsun3
NOL1/NOP2/Sun domain family member 3
IAGP
MGI
PMID:36949224
NCBI chr16:62,552,807...62,607,238
Ensembl chr16:62,552,807...62,607,181
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Nsun4
NOL1/NOP2/Sun domain family, member 4
IAGP
MGI
PMID:24516400
NCBI chr 4:115,890,202...115,911,076
Ensembl chr 4:115,890,039...115,911,073
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Ntmt1
N-terminal Xaa-Pro-Lys N-methyltransferase 1
IAGP
MGI
PMID:25843235
NCBI chr 2:30,697,576...30,713,045
Ensembl chr 2:30,697,838...30,713,045
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Opa1
OPA1, mitochondrial dynamin like GTPase
IAGP
MGI
PMID:23250881 PMID:24055366
NCBI chr16:29,398,099...29,481,924
Ensembl chr16:29,398,152...29,473,702
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Opa3
optic atrophy 3
IAGP
MGI
PMID:18222992 PMID:22869679
NCBI chr 7:18,962,314...18,980,742
Ensembl chr 7:18,962,259...18,990,468
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Otc
ornithine transcarbamylase
IAGP
MGI
PMID:2920015
NCBI chr X:10,118,584...10,187,275
Ensembl chr X:10,118,544...10,187,263
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Pabpn1
poly(A) binding protein, nuclear 1
IAGP
MGI
PMID:28575395
NCBI chr14:55,131,600...55,136,384
Ensembl chr14:55,129,957...55,135,626
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Parl
presenilin associated, rhomboid-like
IAGP
MGI
PMID:16839884 PMID:30578322
NCBI chr16:20,098,570...20,121,090
Ensembl chr16:20,098,568...20,121,137
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Pcx
pyruvate carboxylase
IAGP
MGI
PMID:36441025
NCBI chr19:4,560,500...4,671,780
Ensembl chr19:4,560,500...4,671,780
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Pdap1
PDGFA associated protein 1
IAGP
MGI
PMID:32609329
NCBI chr 5:145,065,580...145,076,835
Ensembl chr 5:145,065,579...145,077,048
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Pdx1
pancreatic and duodenal homeobox 1
IAGP
MGI
PMID:11781323
NCBI chr 5:147,206,907...147,212,658
Ensembl chr 5:147,206,769...147,212,658
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Pex1
peroxisomal biogenesis factor 1
IAGP
MGI
PMID:31207289
NCBI chr 5:3,646,066...3,687,230
Ensembl chr 5:3,646,066...3,687,232
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Pex13
peroxisomal biogenesis factor 13
IAGP
MGI
PMID:20959636
NCBI chr11:23,597,283...23,615,883
Ensembl chr11:23,596,479...23,615,959
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Pex16
peroxisomal biogenesis factor 16
IAGP
MGI
PMID:30511960
NCBI chr 2:92,205,043...92,211,563
Ensembl chr 2:92,205,021...92,211,562
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Pgam5
phosphoglycerate mutase family member 5
IAGP
MGI
PMID:25222142
NCBI chr 5:110,407,001...110,417,765
Ensembl chr 5:110,406,996...110,417,779
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Pik3c3
phosphatidylinositol 3-kinase catalytic subunit type 3
IAGP
MGI
PMID:22592798
NCBI chr18:30,390,441...30,481,179
Ensembl chr18:30,405,800...30,481,179
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Pink1
PTEN induced putative kinase 1
IAGP
MGI
PMID:19492057 PMID:21249202 PMID:21385841
NCBI chr 4:138,040,718...138,053,631
Ensembl chr 4:138,040,720...138,053,618
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Pitrm1
pitrilysin metallepetidase 1
IAGP
MGI
PMID:26697887
NCBI chr13:6,598,158...6,630,194
Ensembl chr13:6,598,185...6,630,551
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Pla2g6
phospholipase A2, group VI
IAGP
MGI
PMID:30088174
NCBI chr15:79,170,428...79,212,915
Ensembl chr15:79,170,428...79,212,590
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Plin3
perilipin 3
IAGP
MGI
PMID:29440067
NCBI chr17:56,585,962...56,597,511
Ensembl chr17:56,584,476...56,599,873
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Pnp
purine-nucleoside phosphorylase
IAGP
MGI
PMID:10859343
NCBI chr14:51,181,760...51,190,869
Ensembl chr14:51,168,539...51,190,869
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Pnpla8
patatin-like phospholipase domain containing 8
IAGP
MGI
PMID:17923475
NCBI chr12:44,315,916...44,362,718
Ensembl chr12:44,268,153...44,369,315
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Pnpt1
polyribonucleotide nucleotidyltransferase 1
IAGP
MGI
PMID:20691904
NCBI chr11:29,080,236...29,112,010
Ensembl chr11:29,080,744...29,111,828
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Polg
polymerase (DNA directed), gamma
IAGP
MGI
PMID:16870370 PMID:19734452 PMID:38570685
NCBI chr 7:79,095,979...79,117,659
Ensembl chr 7:79,095,979...79,116,110
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Polrmt
polymerase (RNA) mitochondrial (DNA directed)
IAGP
MGI
PMID:27532055
NCBI chr10:79,571,951...79,582,436
Ensembl chr10:79,571,957...79,582,415
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Ppargc1a
peroxisome proliferative activated receptor, gamma, coactivator 1 alpha
IAGP
MGI
PMID:17932564 PMID:24280126 PMID:29925537
NCBI chr 5:51,611,591...52,273,316
Ensembl chr 5:51,611,592...51,725,068
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Ppargc1b
peroxisome proliferative activated receptor, gamma, coactivator 1 beta
IAGP
MGI
PMID:17141629 PMID:24049736
NCBI chr18:61,424,516...61,533,846
Ensembl chr18:61,431,207...61,533,502
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Ppif
peptidylprolyl isomerase F (cyclophilin F)
IAGP
MGI
PMID:15792954 PMID:15800626 PMID:15800627 PMID:16103352 PMID:37696137
NCBI chr14:25,693,998...25,700,892
Ensembl chr14:25,694,578...25,700,892
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Pptc7
PTC7 protein phosphatase homolog
IAGP
MGI
PMID:31324765
NCBI chr 5:122,422,461...122,462,344
Ensembl chr 5:122,422,428...122,462,344
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Prdx3
peroxiredoxin 3
IAGP
MGI
PMID:21902452
NCBI chr19:60,852,504...60,862,976
Ensembl chr19:60,852,489...60,862,994
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Prkn
parkin RBR E3 ubiquitin protein ligase
IAGP
MGI
PMID:23152496
NCBI chr17:11,059,227...12,282,257
Ensembl chr17:11,059,271...12,282,248
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Prorp
protein only RNase P catalytic subunit
IAGP
MGI
PMID:27498866
NCBI chr12:55,349,422...55,429,276
Ensembl chr12:55,346,362...55,429,318
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Ptcd1
pentatricopeptide repeat domain 1
IAGP
MGI
PMID:28835921
NCBI chr 5:145,084,188...145,103,914
Ensembl chr 5:145,084,324...145,103,918
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Rab7
RAB7, member RAS oncogene family
IAGP
MGI
PMID:37878717
NCBI chr 6:87,976,088...88,022,252
Ensembl chr 6:87,976,088...88,022,252
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Rangrf
RAN guanine nucleotide release factor
IAGP
MGI
PMID:35533905
NCBI chr11:68,863,310...68,866,011
Ensembl chr11:68,863,310...68,866,011
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Rhot1
ras homolog family member T1
IAGP
MGI
PMID:25136135
NCBI chr11:80,099,844...80,158,736
Ensembl chr11:80,099,845...80,158,733
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Rock1
Rho-associated coiled-coil containing protein kinase 1
IAGP
MGI
PMID:22326220
NCBI chr18:10,064,401...10,182,225
Ensembl chr18:10,064,401...10,182,045
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Romo1
reactive oxygen species modulator 1
IAGP
MGI
PMID:40461459
NCBI chr 2:155,986,073...155,987,714
Ensembl chr 2:155,985,959...155,987,717
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Ryr1
ryanodine receptor 1, skeletal muscle
IAGP
MGI
PMID:25564733
NCBI chr 7:28,702,765...28,824,599
Ensembl chr 7:28,702,769...28,824,604
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Sacs
sacsin
IAGP
MGI
PMID:22307627
NCBI chr14:61,375,870...61,478,142
Ensembl chr14:61,375,906...61,478,144
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Sco1
SCO1 cytochrome c oxidase assembly protein
IAGP
MGI
PMID:25683716
NCBI chr11:66,943,473...66,958,270
Ensembl chr11:66,943,496...66,957,896
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Sdhaf4
succinate dehydrogenase complex assembly factor 4
IAGP
MGI
PMID:35803927
NCBI chr 1:24,035,020...24,044,721
Ensembl chr 1:24,035,020...24,044,737
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Slc25a19
solute carrier family 25 (mitochondrial thiamine pyrophosphate carrier), member 19
IAGP
MGI
PMID:17035501
NCBI chr11:115,504,991...115,519,122
Ensembl chr11:115,505,004...115,519,121
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Slc25a23
solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 23
IAGP
MGI
PMID:23344948
NCBI chr17:57,350,711...57,366,863
Ensembl chr17:57,350,711...57,366,863
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Slc6a3
solute carrier family 6 (neurotransmitter transporter, dopamine), member 3
IAGP
MGI
PMID:21768369 PMID:25609609
NCBI chr13:73,684,270...73,726,791
Ensembl chr13:73,684,866...73,726,791
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Smdt1
single-pass membrane protein with aspartate rich tail 1
IAGP
MGI
PMID:27477272 PMID:32017711
NCBI chr15:82,229,901...82,233,266
Ensembl chr15:82,223,160...82,233,292
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Snph
syntaphilin
IAGP
MGI
PMID:18191227
NCBI chr 2:151,432,469...151,474,527
Ensembl chr 2:151,432,469...151,474,513
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Sod1
superoxide dismutase 1, soluble
IAGP
MGI
PMID:25468678
NCBI chr16:90,017,650...90,023,221
Ensembl chr16:90,017,642...90,023,217
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Sod2
superoxide dismutase 2, mitochondrial
IAGP
MGI
PMID:8790408 PMID:11226230 PMID:11514315 PMID:11677043 PMID:19776389
NCBI chr17:13,226,726...13,237,006
Ensembl chr17:13,225,733...13,258,950
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Speer6-ps1
spermatogenesis associated glutamate (E)-rich protein 6, pseudogene 1
IAGP
MGI
PMID:17464988 PMID:20691904 PMID:24995976 PMID:25683716 PMID:26344103 PMID:27689697 PMID:36441025 More...
NCBI chr13:3,199,475...3,239,678
Ensembl chr13:3,236,206...3,239,317 Ensembl chr13:3,236,206...3,239,317
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Sqstm1
sequestosome 1
IAGP
MGI
PMID:22222206
NCBI chr11:50,090,979...50,105,303
Ensembl chr11:50,090,193...50,101,654
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Sucla2
succinate-Coenzyme A ligase, ADP-forming, beta subunit
IAGP
MGI
PMID:24271779 PMID:27496549
NCBI chr14:73,790,226...73,833,584
Ensembl chr14:73,762,759...73,833,582
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Suclg2
succinate-Coenzyme A ligase, GDP-forming, beta subunit
IAGP
MGI
PMID:27496549
NCBI chr 6:95,449,992...95,695,799
Ensembl chr 6:95,449,990...95,695,781
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Surf1
surfeit gene 1
IAGP
MGI
PMID:17210671
NCBI chr 2:26,803,390...26,806,667
Ensembl chr 2:26,803,393...26,806,542
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Taf7l
TATA-box binding protein associated factor 7 like
IAGP
MGI
PMID:24876128
NCBI chr X:133,360,865...133,377,254
Ensembl chr X:133,360,867...133,377,239
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Tafazzin
tafazzin, phospholipid-lysophospholipid transacylase
IAGP
MGI
PMID:34129362
NCBI chr X:73,325,498...73,340,182
Ensembl chr X:73,325,518...73,333,757
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Tbc1d15
TBC1 domain family, member 15
IAGP
MGI
PMID:35680100
NCBI chr10:115,031,459...115,087,343
Ensembl chr10:115,033,777...115,087,372
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Tex44
testis expressed 44
IAGP
MGI
PMID:38750428
NCBI chr 1:86,354,051...86,355,771
Ensembl chr 1:86,354,051...86,355,774
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Tfam
transcription factor A, mitochondrial
IAGP
MGI
PMID:21768369 PMID:23386745
NCBI chr10:71,061,298...71,074,157
Ensembl chr10:71,061,294...71,074,110
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Tfb2m
transcription factor B2, mitochondrial
IAGP
MGI
PMID:28702322
NCBI chr 1:179,355,617...179,373,870
Ensembl chr 1:179,355,620...179,373,832
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Thbs1
thrombospondin 1
IAGP
MGI
PMID:17293482
NCBI chr 2:117,942,357...117,957,614
Ensembl chr 2:117,942,357...117,957,614
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Tigar
Trp53 induced glycolysis regulatory phosphatase
IAGP
MGI
PMID:22044588
NCBI chr 6:127,062,079...127,086,564
Ensembl chr 6:127,062,079...127,086,520
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Tm9sf5
transmembrane 9 superfamily member 5
IAGP
MGI
PMID:34635817
NCBI chr X:56,446,127...56,534,133
Ensembl chr X:56,454,514...56,534,127
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Tmem135
transmembrane protein 135
IAGP
MGI
PMID:27863209
NCBI chr 7:88,789,230...89,053,911
Ensembl chr 7:88,788,922...89,053,430
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Tmem225
transmembrane protein 225
IAGP
MGI
PMID:38246484
NCBI chr 9:40,059,418...40,062,176
Ensembl chr 9:40,059,418...40,062,170
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Tmem70
transmembrane protein 70
IAGP
MGI
PMID:28173120
NCBI chr 1:16,735,415...16,748,501
Ensembl chr 1:16,735,431...16,748,499
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Tmlhe
trimethyllysine hydroxylase, epsilon
IAGP
MGI
PMID:34728372
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Tmub1
transmembrane and ubiquitin-like domain containing 1
IAGP
MGI
PMID:31867855
NCBI chr 5:24,650,461...24,652,859
Ensembl chr 5:24,650,456...24,652,852
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Top1mt
DNA topoisomerase 1, mitochondrial
IAGP
MGI
PMID:22911747
NCBI chr15:75,528,878...75,551,184
Ensembl chr15:75,528,884...75,550,649
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Trmu
tRNA 5-methylaminomethyl-2-thiouridylate methyltransferase
IAGP
MGI
PMID:27689697
NCBI chr15:85,763,505...85,781,595
Ensembl chr15:85,763,513...85,781,595
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Trp53
transformation related protein 53
IAGP
MGI
PMID:22044588
NCBI chr11:69,471,174...69,482,699
Ensembl chr11:69,471,185...69,482,699
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Trp53inp1
transformation related protein 53 inducible nuclear protein 1
IAGP
MGI
PMID:25828351
NCBI chr 4:11,156,441...11,174,379
Ensembl chr 4:11,156,431...11,174,379
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Trp63
transformation related protein 63
IAGP
MGI
PMID:17079275
NCBI chr16:25,502,513...25,710,842
Ensembl chr16:25,502,513...25,710,852
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Tyk2
tyrosine kinase 2
IAGP
MGI
PMID:23217260
NCBI chr 9:21,015,364...21,042,689
Ensembl chr 9:21,015,364...21,042,539
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Ube3b
ubiquitin protein ligase E3B
IAGP
MGI
PMID:30808755
NCBI chr 5:114,518,578...114,559,226
Ensembl chr 5:114,518,668...114,559,230
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Uchl1
ubiquitin carboxy-terminal hydrolase L1
IAGP
MGI
PMID:39667488
NCBI chr 5:66,833,464...66,844,577
Ensembl chr 5:66,833,434...66,844,577
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Ucp1
uncoupling protein 1 (mitochondrial, proton carrier)
IAGP
MGI
PMID:10497167 PMID:11279075
NCBI chr 8:84,016,977...84,025,085
Ensembl chr 8:84,016,981...84,025,081
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Ucp2
uncoupling protein 2 (mitochondrial, proton carrier)
IAGP
MGI
PMID:15147521 PMID:18054322
NCBI chr 7:100,142,565...100,148,832
Ensembl chr 7:100,142,544...100,151,227
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Ucp3
uncoupling protein 3 (mitochondrial, proton carrier)
IAGP
MGI
PMID:10748195 PMID:11707458
NCBI chr 7:100,122,198...100,135,639
Ensembl chr 7:100,122,197...100,135,639
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Uqcrfs1
ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1
IAGP
MGI
PMID:22914734
NCBI chr13:30,724,295...30,729,299
Ensembl chr13:30,724,291...30,729,345
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Vps35
VPS35 retromer complex component
IAGP
MGI
PMID:33745227
NCBI chr 8:85,987,014...86,026,146
Ensembl chr 8:85,987,021...86,026,431
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Wnt16
wingless-type MMTV integration site family, member 16
IAGP
MGI
PMID:38123514
NCBI chr 6:22,288,179...22,298,521
Ensembl chr 6:22,288,226...22,298,521
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Wwtr1
WW domain containing transcription regulator 1
IAGP
MGI
PMID:38123514
NCBI chr 3:57,363,065...57,483,331
Ensembl chr 3:57,363,070...57,483,331
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Xrcc1
X-ray repair complementing defective repair in Chinese hamster cells 1
IAGP
MGI
PMID:30998386
NCBI chr 7:24,246,124...24,272,863
Ensembl chr 7:24,245,714...24,272,865
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Yap1
yes-associated protein 1
IAGP
MGI
PMID:38123514
NCBI chr 9:7,932,000...8,004,890
Ensembl chr 9:7,932,000...8,004,597
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Yme1l1
YME1-like 1 (S. cerevisiae)
IAGP
MGI
PMID:26785494
NCBI chr 2:23,046,517...23,089,272
Ensembl chr 2:23,046,381...23,089,272
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Zfp106
zinc finger protein 106
IAGP
MGI
PMID:26604141
NCBI chr 2:120,337,303...120,394,345
Ensembl chr 2:120,337,301...120,394,324
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A1cf
APOBEC1 complementation factor
IAGP
MGI
PMID:24658400
NCBI chr19:31,846,156...31,929,765
Ensembl chr19:31,846,164...31,926,395
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Afg3l2
AFG3-like AAA ATPase 2
IAGP
MGI
PMID:19625515
NCBI chr18:67,537,830...67,582,277
Ensembl chr18:67,537,834...67,582,242
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Aifm1
apoptosis-inducing factor, mitochondrion-associated 1
IAGP
MGI
PMID:16287843
NCBI chr X:47,563,821...47,602,440
Ensembl chr X:47,563,821...47,602,440
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Alpl
alkaline phosphatase, liver/bone/kidney
IAGP
MGI
PMID:30998386
NCBI chr 4:137,469,042...137,523,695
Ensembl chr 4:137,469,044...137,523,695
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Atpaf1
ATP synthase mitochondrial F1 complex assembly factor 1
IAGP
MGI
PMID:34375736
NCBI chr 4:115,642,025...115,669,120
Ensembl chr 4:115,642,009...115,679,852
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Bud23
BUD23, rRNA methyltransferase and ribosome maturation factor
IAGP
MGI
PMID:31939735
NCBI chr 5:135,081,811...135,093,813
Ensembl chr 5:135,081,811...135,093,813
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Camkmt
calmodulin-lysine N-methyltransferase
IAGP
MGI
PMID:26247364
NCBI chr17:85,397,989...85,766,017
Ensembl chr17:85,397,980...85,766,016
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Cdk5rap1
CDK5 regulatory subunit associated protein 1
IAGP
MGI
PMID:25738458
NCBI chr 2:154,063,931...154,216,170
Ensembl chr 2:154,177,300...154,214,930
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Chchd4
coiled-coil-helix-coiled-coil-helix domain containing 4
IAGP
MGI
PMID:26004228
NCBI chr 6:91,441,258...91,450,405
Ensembl chr 6:91,439,154...91,450,528
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Cisd1
CDGSH iron sulfur domain 1
IAGP
MGI
PMID:17376863
NCBI chr10:71,166,324...71,180,679
Ensembl chr10:71,166,310...71,180,784
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Coq9
coenzyme Q9
IAGP
MGI
PMID:23255162
NCBI chr 8:95,565,041...95,581,523
Ensembl chr 8:95,564,949...95,581,523
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Cox17
cytochrome c oxidase assembly protein 17, copper chaperone
IAGP
MGI
PMID:12370308
NCBI chr16:38,167,332...38,173,125
Ensembl chr16:38,167,353...38,182,659
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Dguok
deoxyguanosine kinase
IAGP
MGI
PMID:31127938
NCBI chr 6:83,457,199...83,483,887
Ensembl chr 6:83,457,199...83,483,951
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Dnajc15
DnaJ heat shock protein family (Hsp40) member C15
IAGP
MGI
PMID:23530063
NCBI chr14:78,063,657...78,112,357
Ensembl chr14:78,058,121...78,112,565
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Dnm1l
dynamin 1-like
IAGP
MGI
PMID:20585624
NCBI chr16:16,130,092...16,176,863
Ensembl chr16:16,130,094...16,176,823
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Elac2
elaC ribonuclease Z 2
IAGP
MGI
PMID:30126926
NCBI chr11:64,869,856...64,892,906
Ensembl chr11:64,869,864...64,892,895
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Elavl1
ELAV like RNA binding protein 1
IAGP
MGI
PMID:31519904
NCBI chr 8:4,334,781...4,375,104
Ensembl chr 8:4,335,382...4,375,413
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Fmc1
formation of mitochondrial complex V assembly factor 1
IAGP
MGI
PMID:29371327
NCBI chr 6:38,511,796...38,516,384
Ensembl chr 6:38,510,437...38,516,384
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Gamt
guanidinoacetate methyltransferase
IAGP
MGI
PMID:15028668
NCBI chr10:80,093,985...80,096,846
Ensembl chr10:80,093,985...80,096,846
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Gt(ROSA)26Sor
gene trap ROSA 26, Philippe Soriano
IAGP
MGI
PMID:33753492
NCBI chr 6:113,044,389...113,054,205
Ensembl chr 6:113,043,843...113,055,336
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Hacd2
3-hydroxyacyl-CoA dehydratase 2
IAGP
MGI
PMID:36693621
NCBI chr16:34,842,791...34,929,560
Ensembl chr16:34,842,798...34,929,547
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Hoxa11os
homeobox A11, opposite strand
IAGP
MGI
PMID:37494932
NCBI chr 6:52,222,013...52,226,770
Ensembl chr 6:52,220,356...52,226,784
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Hspd1
heat shock protein 1 (chaperonin)
IAGP
MGI
PMID:23466696
NCBI chr 1:55,116,992...55,127,402
Ensembl chr 1:55,116,994...55,127,402
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Ide
insulin degrading enzyme
IAGP
MGI
PMID:30807788
NCBI chr19:37,246,140...37,341,664
Ensembl chr19:37,246,142...37,340,010
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Immt
inner membrane protein, mitochondrial
IAGP
MGI
PMID:36974636
NCBI chr 6:71,806,200...71,852,250
Ensembl chr 6:71,808,315...71,854,372
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Kcna1
potassium voltage-gated channel, shaker-related subfamily, member 1
IAGP
MGI
PMID:24270080
NCBI chr 6:126,613,426...126,622,764
Ensembl chr 6:126,617,360...126,623,347
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Lclat1
lysocardiolipin acyltransferase 1
IAGP
MGI
PMID:20674860
NCBI chr17:73,414,980...73,550,363
Ensembl chr17:73,414,980...73,550,363
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Lmna
lamin A
IAGP
MGI
PMID:21818413
NCBI chr 3:88,388,455...88,413,842
Ensembl chr 3:88,387,454...88,417,263
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Mff
mitochondrial fission factor
IAGP
MGI
PMID:33476744
NCBI chr 1:82,702,599...82,730,111
Ensembl chr 1:82,702,611...82,730,115
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Mfn1
mitofusin 1
IAGP
MGI
PMID:33674260
NCBI chr 3:32,583,594...32,633,384
Ensembl chr 3:32,583,614...32,633,388
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Mfn2
mitofusin 2
IAGP
MGI
PMID:33674260
NCBI chr 4:147,958,043...147,989,527
Ensembl chr 4:147,958,056...147,989,161
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Mrpl22
mitochondrial ribosomal protein L22
IAGP
MGI
PMID:32376682
NCBI chr11:58,060,850...58,070,406
Ensembl chr11:58,062,487...58,070,391
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Mrpl3
mitochondrial ribosomal protein L3
IAGP
MGI
PMID:32376682
NCBI chr 9:104,930,394...104,954,665
Ensembl chr 9:104,930,438...104,957,087
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Mrpl44
mitochondrial ribosomal protein L44
IAGP
MGI
PMID:32376682
NCBI chr 1:79,753,735...79,759,162
Ensembl chr 1:79,753,735...79,759,162
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Mrps12
mitochondrial ribosomal protein S12
IAGP
MGI
PMID:31721250
NCBI chr 7:28,439,066...28,441,246
Ensembl chr 7:28,439,066...28,441,245
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Mrps18c
mitochondrial ribosomal protein S18C
IAGP
MGI
PMID:32376682
NCBI chr 5:100,946,625...100,952,333
Ensembl chr 5:100,946,493...100,952,337
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Mrps22
mitochondrial ribosomal protein S22
IAGP
MGI
PMID:32376682
NCBI chr 9:98,470,783...98,483,732
Ensembl chr 9:98,470,783...98,483,713
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Mrps34
mitochondrial ribosomal protein S34
IAGP
MGI
PMID:25816300
NCBI chr17:25,114,094...25,115,263
Ensembl chr17:25,114,090...25,116,476
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mt-Co1
cytochrome c oxidase I, mitochondrial
IAGP
MGI
PMID:16449238 PMID:18276892
NCBI chr MT:5,328...6,872
Ensembl chr MT:5,328...6,872
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mt-Nd6
NADH dehydrogenase 6, mitochondrial
IAGP
MGI
PMID:18276892 PMID:20674568
NCBI chr MT:13,552...14,070
Ensembl chr MT:13,552...14,070
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Mterf2
mitochondrial transcription termination factor 2
IAGP
MGI
PMID:19490905
NCBI chr10:84,951,092...84,963,982
Ensembl chr10:84,955,297...84,963,891
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Mterf3
mitochondrial transcription termination factor 3
IAGP
MGI
PMID:17662942
NCBI chr13:67,053,520...67,081,148
Ensembl chr13:67,055,032...67,081,152
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Mtfr1
mitochondrial fission regulator 1
IAGP
MGI
PMID:20568109
NCBI chr 3:19,241,481...19,274,981
Ensembl chr 3:19,241,491...19,274,981
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Mtg1
mitochondrial ribosome-associated GTPase 1
IAGP
MGI
PMID:30707992
NCBI chr 7:139,717,477...139,730,699
Ensembl chr 7:139,717,477...139,730,699
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Ndufaf2
NADH:ubiquinone oxidoreductase complex assembly factor 2
IAGP
MGI
PMID:23702311
NCBI chr13:108,189,123...108,295,189
Ensembl chr13:108,139,249...108,295,157
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Ndufs4
NADH:ubiquinone oxidoreductase core subunit S4
IAGP
MGI
PMID:18396137 PMID:23702311
NCBI chr13:114,424,331...114,524,630
Ensembl chr13:114,424,331...114,524,794
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Noa1
nitric oxide associated 1
IAGP
MGI
PMID:21118999
NCBI chr 5:77,442,016...77,458,276
Ensembl chr 5:77,442,029...77,457,931
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Obscn
obscurin, cytoskeletal calmodulin and titin-interacting RhoGEF
IAGP
MGI
PMID:31098411
NCBI chr11:58,885,082...59,027,201
Ensembl chr11:58,885,082...59,029,996
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Obsl1
obscurin-like 1
IAGP
MGI
PMID:31098411
NCBI chr 1:75,462,469...75,483,134
Ensembl chr 1:75,455,954...75,483,096
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Pax7
paired box 7
IAGP
MGI
PMID:33753492
NCBI chr 4:139,464,357...139,560,841
Ensembl chr 4:139,464,373...139,560,839
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Paxbp1
PAX3 and PAX7 binding protein 1
IAGP
MGI
PMID:33753492
NCBI chr16:90,810,925...90,841,267
Ensembl chr16:90,810,925...90,841,431
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Pdss2
prenyl (solanesyl) diphosphate synthase, subunit 2
IAGP
MGI
PMID:18437205 PMID:23150520
NCBI chr10:43,095,396...43,340,878
Ensembl chr10:43,097,482...43,340,878
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Pex5
peroxisomal biogenesis factor 5
IAGP
MGI
PMID:15732085
NCBI chr 6:124,373,774...124,392,878
Ensembl chr 6:124,373,775...124,392,026
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Pink1
PTEN induced putative kinase 1
IAGP
MGI
PMID:19285945 PMID:19492057
NCBI chr 4:138,040,718...138,053,631
Ensembl chr 4:138,040,720...138,053,618
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Pnpt1
polyribonucleotide nucleotidyltransferase 1
IAGP
MGI
PMID:20691904
NCBI chr11:29,080,236...29,112,010
Ensembl chr11:29,080,744...29,111,828
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Polg
polymerase (DNA directed), gamma
IAGP
MGI
PMID:15164064
NCBI chr 7:79,095,979...79,117,659
Ensembl chr 7:79,095,979...79,116,110
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Pon3
paraoxonase 3
IAGP
MGI
PMID:25477283
NCBI chr 6:5,216,253...5,256,236
Ensembl chr 6:5,220,852...5,256,286
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Prdx5
peroxiredoxin 5
IAGP
MGI
PMID:30044981
NCBI chr19:6,884,065...6,887,474
Ensembl chr19:6,884,065...6,887,474
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Prkn
parkin RBR E3 ubiquitin protein ligase
IAGP
MGI
PMID:17412759
NCBI chr17:11,059,227...12,282,257
Ensembl chr17:11,059,271...12,282,248
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Prorp
protein only RNase P catalytic subunit
IAGP
MGI
PMID:27498866
NCBI chr12:55,349,422...55,429,276
Ensembl chr12:55,346,362...55,429,318
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Prss55
serine protease 55
IAGP
MGI
PMID:33417308
NCBI chr14:64,312,884...64,338,445
Ensembl chr14:64,312,887...64,327,611
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Ptcd2
pentatricopeptide repeat domain 2
IAGP
MGI
PMID:18729827
NCBI chr13:99,456,157...99,481,215
Ensembl chr13:99,456,155...99,481,213
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Sco2
SCO2 cytochrome c oxidase assembly protein
IAGP
MGI
PMID:19837698
NCBI chr15:89,255,833...89,258,094
Ensembl chr15:89,255,840...89,258,049
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Slc16a13
solute carrier family 16 (monocarboxylic acid transporters), member 13
IAGP
MGI
PMID:34211098
NCBI chr11:70,107,615...70,113,638
Ensembl chr11:70,107,615...70,111,890
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Slc25a3
solute carrier family 25 (mitochondrial carrier, phosphate carrier), member 3
IAGP
MGI
PMID:24658400
NCBI chr10:90,952,436...90,959,902
Ensembl chr10:90,952,436...90,959,921
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Slc25a48
solute carrier family 25, member 48
IAGP
MGI
PMID:39111307
NCBI chr13:56,585,774...56,620,180
Ensembl chr13:56,586,168...56,622,052
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Sod2
superoxide dismutase 2, mitochondrial
IAGP
MGI
PMID:16959785 PMID:26240345
NCBI chr17:13,226,726...13,237,006
Ensembl chr17:13,225,733...13,258,950
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Speer6-ps1
spermatogenesis associated glutamate (E)-rich protein 6, pseudogene 1
IAGP
MGI
PMID:15732085 PMID:20691904 PMID:37524868
NCBI chr13:3,199,475...3,239,678
Ensembl chr13:3,236,206...3,239,317 Ensembl chr13:3,236,206...3,239,317
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Sqstm1
sequestosome 1
IAGP
MGI
PMID:23257354
NCBI chr11:50,090,979...50,105,303
Ensembl chr11:50,090,193...50,101,654
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Tefm
transcription elongation factor, mitochondrial
IAGP
MGI
PMID:31036713
NCBI chr11:80,027,500...80,033,697
Ensembl chr11:80,027,504...80,033,001
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Tfam
transcription factor A, mitochondrial
IAGP
MGI
PMID:11259653
NCBI chr10:71,061,298...71,074,157
Ensembl chr10:71,061,294...71,074,110
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Tfb2m
transcription factor B2, mitochondrial
IAGP
MGI
PMID:28702322
NCBI chr 1:179,355,617...179,373,870
Ensembl chr 1:179,355,620...179,373,832
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Tgm2
transglutaminase 2, C polypeptide
IAGP
MGI
PMID:16528383 PMID:18250473
NCBI chr 2:157,958,325...157,988,312
Ensembl chr 2:157,958,322...157,988,356
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Thra
thyroid hormone receptor alpha
IAGP
MGI
PMID:21914860
NCBI chr11:98,631,539...98,659,832
Ensembl chr11:98,631,464...98,659,832
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Thrap3
thyroid hormone receptor associated protein 3
IAGP
MGI
PMID:37524868
NCBI chr 4:126,057,875...126,096,548
Ensembl chr 4:126,057,875...126,096,553
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Tk2
thymidine kinase 2, mitochondrial
IAGP
MGI
PMID:18467430
NCBI chr 8:104,953,323...104,975,224
Ensembl chr 8:104,953,317...104,975,190
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Tmprss12
transmembrane (C-terminal) protease, serine 12
IAGP
MGI
PMID:35547804
NCBI chr15:100,178,743...100,190,943
Ensembl chr15:100,178,718...100,190,947
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Tppp2
tubulin polymerization-promoting protein family member 2
IAGP
MGI
PMID:30680919
NCBI chr14:52,155,887...52,158,161
Ensembl chr14:52,155,882...52,158,157
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Tspo
translocator protein
IAGP
MGI
PMID:25406832
NCBI chr15:83,447,774...83,458,404
Ensembl chr15:83,447,793...83,458,404
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Tymp
thymidine phosphorylase
IAGP
MGI
PMID:19028666
NCBI chr15:89,255,834...89,261,282
Ensembl chr15:89,256,134...89,261,242
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Ucp3
uncoupling protein 3 (mitochondrial, proton carrier)
IAGP
MGI
PMID:11274222
NCBI chr 7:100,122,198...100,135,639
Ensembl chr 7:100,122,197...100,135,639
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Upp1
uridine phosphorylase 1
IAGP
MGI
PMID:19028666
NCBI chr11:9,068,008...9,086,170
Ensembl chr11:9,068,103...9,086,170
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Wdr45
WD repeat domain 45
IAGP
MGI
PMID:34043061
NCBI chr X:7,588,212...7,594,439
Ensembl chr X:7,580,572...7,594,445
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Xrcc1
X-ray repair complementing defective repair in Chinese hamster cells 1
IAGP
MGI
PMID:30998386
NCBI chr 7:24,246,124...24,272,863
Ensembl chr 7:24,245,714...24,272,865
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Zfp106
zinc finger protein 106
IAGP
MGI
PMID:26604141
NCBI chr 2:120,337,303...120,394,345
Ensembl chr 2:120,337,301...120,394,324
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Fxn
frataxin
IAGP
MGI
PMID:28444186
NCBI chr19:24,236,909...24,257,954
Ensembl chr19:24,238,817...24,257,969
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Ins1
insulin I
IAGP
MGI
PMID:39379383
NCBI chr19:52,252,735...52,253,453
Ensembl chr19:52,252,735...52,253,914
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Med15
mediator complex subunit 15
IAGP
MGI
PMID:39379383
NCBI chr16:17,469,072...17,540,811
Ensembl chr16:17,469,072...17,550,755
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Pptc7
PTC7 protein phosphatase homolog
IAGP
MGI
PMID:31324765
NCBI chr 5:122,422,461...122,462,344
Ensembl chr 5:122,422,428...122,462,344
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Rangrf
RAN guanine nucleotide release factor
IAGP
MGI
PMID:35533905
NCBI chr11:68,863,310...68,866,011
Ensembl chr11:68,863,310...68,866,011
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Lrrk2
leucine-rich repeat kinase 2
IAGP
MGI
PMID:25836420
NCBI chr15:91,556,994...91,700,327
Ensembl chr15:91,557,378...91,700,323
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Serac1
serine active site containing 1
IAGP
MGI
PMID:35235340
NCBI chr17:6,090,846...6,130,064
Ensembl chr17:6,092,471...6,130,016
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4930590J08Rik
RIKEN cDNA 4930590J08 gene
IAGP
MGI
PMID:36331537
NCBI chr 6:91,877,732...91,928,717
Ensembl chr 6:91,879,790...91,927,706
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A1cf
APOBEC1 complementation factor
IAGP
MGI
PMID:26356605
NCBI chr19:31,846,156...31,929,765
Ensembl chr19:31,846,164...31,926,395
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Abcg2
ATP binding cassette subfamily G member 2 (Junior blood group)
IAGP
MGI
PMID:23954234
NCBI chr 6:58,561,476...58,669,436
Ensembl chr 6:58,561,508...58,672,661
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Angel2
angel homolog 2
IAGP
MGI
PMID:36180430
NCBI chr 1:190,657,305...190,679,160
Ensembl chr 1:190,657,309...190,679,159
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Atad3a
ATPase family, AAA domain containing 3A
IAGP
MGI
PMID:29898916
NCBI chr 4:155,825,097...155,845,579
Ensembl chr 4:155,825,098...155,845,550
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Atpaf1
ATP synthase mitochondrial F1 complex assembly factor 1
IAGP
MGI
PMID:34375736
NCBI chr 4:115,642,025...115,669,120
Ensembl chr 4:115,642,009...115,679,852
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Birc5
baculoviral IAP repeat-containing 5
IAGP
MGI
PMID:12145814
NCBI chr11:117,740,063...117,746,569
Ensembl chr11:117,740,077...117,746,569
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Bud23
BUD23, rRNA methyltransferase and ribosome maturation factor
IAGP
MGI
PMID:31939735
NCBI chr 5:135,081,811...135,093,813
Ensembl chr 5:135,081,811...135,093,813
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Cdk5rap1
CDK5 regulatory subunit associated protein 1
IAGP
MGI
PMID:25738458
NCBI chr 2:154,063,931...154,216,170
Ensembl chr 2:154,177,300...154,214,930
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Coq6
coenzyme Q6 monooxygenase
IAGP
MGI
PMID:39496954
NCBI chr12:84,408,530...84,420,570
Ensembl chr12:84,408,431...84,420,570
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Cox7a2l
cytochrome c oxidase subunit 7A2 like
IAGP
MGI
PMID:23857330
NCBI chr17:83,809,346...83,821,762
Ensembl chr17:83,809,347...83,824,759
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Cyct
cytochrome c, testis
IAGP
MGI
PMID:12101247
NCBI chr 2:76,184,286...76,190,797
Ensembl chr 2:76,184,286...76,190,794
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Elac2
elaC ribonuclease Z 2
IAGP
MGI
PMID:30126926
NCBI chr11:64,869,856...64,892,906
Ensembl chr11:64,869,864...64,892,895
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Etfdh
electron transferring flavoprotein, dehydrogenase
IAGP
MGI
PMID:38243131
NCBI chr 3:79,511,095...79,536,074
Ensembl chr 3:79,511,095...79,536,807
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Fars2
phenylalanine-tRNA synthetase 2, mitochondrial
IAGP
MGI
PMID:35794642
NCBI chr13:36,301,373...36,721,569
Ensembl chr13:36,301,395...36,910,254
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Fbxl4
F-box and leucine-rich repeat protein 4
IAGP
MGI
PMID:32525278
NCBI chr 4:22,357,526...22,434,091
Ensembl chr 4:22,357,543...22,434,091
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Gt(ROSA)26Sor
gene trap ROSA 26, Philippe Soriano
IAGP
MGI
PMID:26356605 PMID:33753492
NCBI chr 6:113,044,389...113,054,205
Ensembl chr 6:113,043,843...113,055,336
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Hacd2
3-hydroxyacyl-CoA dehydratase 2
IAGP
MGI
PMID:36693621
NCBI chr16:34,842,791...34,929,560
Ensembl chr16:34,842,798...34,929,547
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Hoxa11os
homeobox A11, opposite strand
IAGP
MGI
PMID:37494932
NCBI chr 6:52,222,013...52,226,770
Ensembl chr 6:52,220,356...52,226,784
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Ido1
indoleamine 2,3-dioxygenase 1
IAGP
MGI
PMID:30478397
NCBI chr 8:25,074,148...25,086,987
Ensembl chr 8:25,074,152...25,087,025
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Immt
inner membrane protein, mitochondrial
IAGP
MGI
PMID:36974636
NCBI chr 6:71,806,200...71,852,250
Ensembl chr 6:71,808,315...71,854,372
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Lacc1
laccase domain containing 1
IAGP
MGI
PMID:27478939
NCBI chr14:77,261,640...77,274,344
Ensembl chr14:77,261,640...77,274,344
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Mtln
mitoregulin
IAGP
MGI
PMID:29949756
NCBI chr 2:127,633,302...127,634,408
Ensembl chr 2:127,633,308...127,634,408
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Myl1
myosin, light polypeptide 1
IAGP
MGI
PMID:29898916
NCBI chr 1:66,963,454...66,987,091
Ensembl chr 1:66,963,454...66,984,563
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Npl
N-acetylneuraminate pyruvate lyase
IAGP
MGI
PMID:37390204
NCBI chr 1:153,378,762...153,425,460
Ensembl chr 1:153,378,761...153,425,791
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Nsun4
NOL1/NOP2/Sun domain family, member 4
IAGP
MGI
PMID:24516400
NCBI chr 4:115,890,202...115,911,076
Ensembl chr 4:115,890,039...115,911,073
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Pabpn1
poly(A) binding protein, nuclear 1
IAGP
MGI
PMID:28575395
NCBI chr14:55,131,600...55,136,384
Ensembl chr14:55,129,957...55,135,626
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Pax7
paired box 7
IAGP
MGI
PMID:33753492
NCBI chr 4:139,464,357...139,560,841
Ensembl chr 4:139,464,373...139,560,839
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Paxbp1
PAX3 and PAX7 binding protein 1
IAGP
MGI
PMID:33753492
NCBI chr16:90,810,925...90,841,267
Ensembl chr16:90,810,925...90,841,431
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Polg
polymerase (DNA directed), gamma
IAGP
MGI
PMID:23418460
NCBI chr 7:79,095,979...79,117,659
Ensembl chr 7:79,095,979...79,116,110
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Ppargc1b
peroxisome proliferative activated receptor, gamma, coactivator 1 beta
IAGP
MGI
PMID:24049736
NCBI chr18:61,424,516...61,533,846
Ensembl chr18:61,431,207...61,533,502
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Ptcd1
pentatricopeptide repeat domain 1
IAGP
MGI
PMID:28835921
NCBI chr 5:145,084,188...145,103,914
Ensembl chr 5:145,084,324...145,103,918
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Qprt
quinolinate phosphoribosyltransferase
IAGP
MGI
PMID:30478397
NCBI chr 7:126,706,942...126,721,201
Ensembl chr 7:126,706,286...126,721,398
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Rbm43
RNA binding motif protein 43
IAGP
MGI
PMID:39965564
NCBI chr 2:51,814,460...51,825,175
Ensembl chr 2:51,814,460...51,825,175
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Rpl13a
ribosomal protein L13A
IAGP
MGI
PMID:27820699
NCBI chr 7:44,774,987...44,778,169
Ensembl chr 7:44,774,982...44,778,185
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Serac1
serine active site containing 1
IAGP
MGI
PMID:35235340
NCBI chr17:6,090,846...6,130,064
Ensembl chr17:6,092,471...6,130,016
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Slc25a28
solute carrier family 25, member 28
IAGP
MGI
PMID:32518166
NCBI chr19:43,652,240...43,663,320
Ensembl chr19:43,652,240...43,663,320
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Slc25a37
solute carrier family 25, member 37
IAGP
MGI
PMID:32518166
NCBI chr14:69,479,297...69,522,993
Ensembl chr14:69,479,297...69,522,561
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Sod2
superoxide dismutase 2, mitochondrial
IAGP
MGI
PMID:16959785
NCBI chr17:13,226,726...13,237,006
Ensembl chr17:13,225,733...13,258,950
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Speer6-ps1
spermatogenesis associated glutamate (E)-rich protein 6, pseudogene 1
IAGP
MGI
PMID:32518166
NCBI chr13:3,199,475...3,239,678
Ensembl chr13:3,236,206...3,239,317 Ensembl chr13:3,236,206...3,239,317
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Stim1
stromal interaction molecule 1
IAGP
MGI
PMID:34359900
NCBI chr 7:101,909,279...102,086,525
Ensembl chr 7:101,917,013...102,086,526
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Sucla2
succinate-Coenzyme A ligase, ADP-forming, beta subunit
IAGP
MGI
PMID:27496549
NCBI chr14:73,790,226...73,833,584
Ensembl chr14:73,762,759...73,833,582
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Suclg2
succinate-Coenzyme A ligase, GDP-forming, beta subunit
IAGP
MGI
PMID:27496549
NCBI chr 6:95,449,992...95,695,799
Ensembl chr 6:95,449,990...95,695,781
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Tmem70
transmembrane protein 70
IAGP
MGI
PMID:28173120
NCBI chr 1:16,735,415...16,748,501
Ensembl chr 1:16,735,431...16,748,499
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Trap1
TNF receptor-associated protein 1
IAGP
MGI
PMID:25088416
NCBI chr16:3,857,835...3,895,704
Ensembl chr16:3,857,835...3,895,691
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Trp53inp1
transformation related protein 53 inducible nuclear protein 1
IAGP
MGI
PMID:25828351
NCBI chr 4:11,156,441...11,174,379
Ensembl chr 4:11,156,431...11,174,379
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Tusc2
tumor suppressor 2, mitochondrial calcium regulator
IAGP
MGI
PMID:28351997
NCBI chr 9:107,440,454...107,443,307
Ensembl chr 9:107,440,454...107,443,311
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A1cf
APOBEC1 complementation factor
IAGP
MGI
PMID:26356605
NCBI chr19:31,846,156...31,929,765
Ensembl chr19:31,846,164...31,926,395
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Abcg2
ATP binding cassette subfamily G member 2 (Junior blood group)
IAGP
MGI
PMID:23954234
NCBI chr 6:58,561,476...58,669,436
Ensembl chr 6:58,561,508...58,672,661
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Adipoq
adiponectin, C1Q and collagen domain containing
IAGP
MGI
PMID:24531262
NCBI chr16:22,965,286...22,976,718
Ensembl chr16:22,965,286...22,976,778
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Afg3l2
AFG3-like AAA ATPase 2
IAGP
MGI
PMID:18337413 PMID:19625515
NCBI chr18:67,537,830...67,582,277
Ensembl chr18:67,537,834...67,582,242
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Aifm1
apoptosis-inducing factor, mitochondrion-associated 1
IAGP
MGI
PMID:16287843 PMID:16788063 PMID:18791645
NCBI chr X:47,563,821...47,602,440
Ensembl chr X:47,563,821...47,602,440
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Angel2
angel homolog 2
IAGP
MGI
PMID:36180430
NCBI chr 1:190,657,305...190,679,160
Ensembl chr 1:190,657,309...190,679,159
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Apaf1
apoptotic peptidase activating factor 1
IAGP
MGI
PMID:9753321
NCBI chr10:90,825,173...90,918,688
Ensembl chr10:90,825,173...90,918,632
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C1qbp
complement component 1, q subcomponent binding protein
IAGP
MGI
PMID:22904065
NCBI chr11:70,868,672...70,873,852
Ensembl chr11:70,868,662...70,873,852
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Casp9
caspase 9
IAGP
MGI
PMID:9708736
NCBI chr 4:141,520,923...141,543,289
Ensembl chr 4:141,520,923...141,543,287
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Cav1
caveolin 1, caveolae protein
IAGP
MGI
PMID:22326219
NCBI chr 6:17,306,387...17,341,323
Ensembl chr 6:17,306,334...17,341,451
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Cdk5rap1
CDK5 regulatory subunit associated protein 1
IAGP
MGI
PMID:25738458
NCBI chr 2:154,063,931...154,216,170
Ensembl chr 2:154,177,300...154,214,930
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Chchd10
coiled-coil-helix-coiled-coil-helix domain containing 10
IAGP
MGI
PMID:29112723
NCBI chr10:75,768,964...75,773,584
Ensembl chr10:75,768,964...75,773,581
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Chdh
choline dehydrogenase
IAGP
MGI
PMID:20371614
NCBI chr14:29,730,957...29,762,423
Ensembl chr14:29,730,980...29,762,484
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Cisd2
CDGSH iron sulfur domain 2
IAGP
MGI
PMID:19451219
NCBI chr 3:135,112,173...135,129,194
Ensembl chr 3:135,112,173...135,129,686
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Coa8
cytochrome c oxidase assembly factor 8
IAGP
MGI
PMID:30552096
NCBI chr12:111,679,394...111,721,491
Ensembl chr12:111,679,695...111,721,487
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Coq6
coenzyme Q6 monooxygenase
IAGP
MGI
PMID:39496954
NCBI chr12:84,408,530...84,420,570
Ensembl chr12:84,408,431...84,420,570
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Coq7
demethyl-Q 7
IAGP
MGI
PMID:23847050
NCBI chr 7:118,108,881...118,132,529
Ensembl chr 7:118,108,882...118,132,579
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Cox7a2l
cytochrome c oxidase subunit 7A2 like
IAGP
MGI
PMID:23812712
NCBI chr17:83,809,346...83,821,762
Ensembl chr17:83,809,347...83,824,759
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Crls1
cardiolipin synthase 1
IAGP
MGI
PMID:29861389
NCBI chr 2:132,688,557...132,708,706
Ensembl chr 2:132,688,586...132,708,705
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Dnaja3
DnaJ heat shock protein family (Hsp40) member A3
IAGP
MGI
PMID:16327803
NCBI chr16:4,501,934...4,525,559
Ensembl chr16:4,457,853...4,525,559
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Esrrg
estrogen-related receptor gamma
IAGP
MGI
PMID:17618853
NCBI chr 1:187,340,707...187,947,082
Ensembl chr 1:187,340,988...187,947,082
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Fxn
frataxin
IAGP
MGI
PMID:11175786 PMID:15028670 PMID:16919418
NCBI chr19:24,236,909...24,257,954
Ensembl chr19:24,238,817...24,257,969
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Gt(ROSA)26Sor
gene trap ROSA 26, Philippe Soriano
IAGP
MGI
PMID:26356605 PMID:33753492
NCBI chr 6:113,044,389...113,054,205
Ensembl chr 6:113,043,843...113,055,336
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Hccs
holocytochrome c synthetase
IAGP
MGI
PMID:18854137
NCBI chr X:168,094,526...168,103,361
Ensembl chr X:168,033,189...168,103,368
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Hint2
histidine triad nucleotide binding protein 2
IAGP
MGI
PMID:22961760
NCBI chr 4:43,654,227...43,656,445
Ensembl chr 4:43,654,227...43,656,466
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Htra2
HtrA serine peptidase 2
IAGP
MGI
PMID:25531304
NCBI chr 6:83,028,247...83,031,552
Ensembl chr 6:83,028,247...83,032,254
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Immp2l
IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae)
IAGP
MGI
PMID:18094351
NCBI chr12:41,074,060...42,002,371
Ensembl chr12:41,074,089...42,002,371
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Lep
leptin
IAGP
MGI
PMID:16246967
NCBI chr 6:29,060,220...29,073,875
Ensembl chr 6:29,060,219...29,073,876
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Lepr
leptin receptor
IAGP
MGI
PMID:16443782
NCBI chr 4:101,574,393...101,676,375
Ensembl chr 4:101,574,601...101,672,549
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Lmna
lamin A
IAGP
MGI
PMID:36583724
NCBI chr 3:88,388,455...88,413,842
Ensembl chr 3:88,387,454...88,417,263
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Mfn1
mitofusin 1
IAGP
MGI
PMID:17693261
NCBI chr 3:32,583,594...32,633,384
Ensembl chr 3:32,583,614...32,633,388
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Mfn2
mitofusin 2
IAGP
MGI
PMID:17693261 PMID:22914740
NCBI chr 4:147,958,043...147,989,527
Ensembl chr 4:147,958,056...147,989,161
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Mmut
methylmalonyl-Coenzyme A mutase
IAGP
MGI
PMID:19088183
NCBI chr17:41,245,576...41,272,880
Ensembl chr17:41,245,576...41,272,879
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Mrpl22
mitochondrial ribosomal protein L22
IAGP
MGI
PMID:32376682
NCBI chr11:58,060,850...58,070,406
Ensembl chr11:58,062,487...58,070,391
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Mrpl3
mitochondrial ribosomal protein L3
IAGP
MGI
PMID:32376682
NCBI chr 9:104,930,394...104,954,665
Ensembl chr 9:104,930,438...104,957,087
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Mrpl44
mitochondrial ribosomal protein L44
IAGP
MGI
PMID:32376682
NCBI chr 1:79,753,735...79,759,162
Ensembl chr 1:79,753,735...79,759,162
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Mrps18c
mitochondrial ribosomal protein S18C
IAGP
MGI
PMID:32376682
NCBI chr 5:100,946,625...100,952,333
Ensembl chr 5:100,946,493...100,952,337
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Mrps22
mitochondrial ribosomal protein S22
IAGP
MGI
PMID:32376682
NCBI chr 9:98,470,783...98,483,732
Ensembl chr 9:98,470,783...98,483,713
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mt-Nd6
NADH dehydrogenase 6, mitochondrial
IAGP
MGI
PMID:23129651 PMID:27626666
NCBI chr MT:13,552...14,070
Ensembl chr MT:13,552...14,070
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mt-Ta
tRNA alanine, mitochondrial
IAGP
MGI
PMID:27626666
NCBI chr MT:5,018...5,086
Ensembl chr MT:5,018...5,086
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mt-Tk
tRNA lysine, mitochondrial
IAGP
MGI
PMID:24510903
NCBI chr MT:7,700...7,764
Ensembl chr MT:7,700...7,764
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Myl1
myosin, light polypeptide 1
IAGP
MGI
PMID:12417746
NCBI chr 1:66,963,454...66,987,091
Ensembl chr 1:66,963,454...66,984,563
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Ndufa5
NADH:ubiquinone oxidoreductase subunit A5
IAGP
MGI
PMID:24154540
NCBI chr 6:24,518,661...24,527,689
Ensembl chr 6:24,518,665...24,528,012
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Ndufs4
NADH:ubiquinone oxidoreductase core subunit S4
IAGP
MGI
PMID:19460290 PMID:20534480
NCBI chr13:114,424,331...114,524,630
Ensembl chr13:114,424,331...114,524,794
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Ndufs6
NADH:ubiquinone oxidoreductase core subunit S6
IAGP
MGI
PMID:22474353
NCBI chr13:73,467,995...73,476,574
Ensembl chr13:73,467,957...73,476,661
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Nkx2-5
NK2 homeobox 5
IAGP
MGI
PMID:18854137
NCBI chr17:27,057,638...27,063,962
Ensembl chr17:27,057,638...27,063,983
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Opa1
OPA1, mitochondrial dynamin like GTPase
IAGP
MGI
PMID:21551073
NCBI chr16:29,398,099...29,481,924
Ensembl chr16:29,398,152...29,473,702
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Parl
presenilin associated, rhomboid-like
IAGP
MGI
PMID:30578322
NCBI chr16:20,098,570...20,121,090
Ensembl chr16:20,098,568...20,121,137
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Pax7
paired box 7
IAGP
MGI
PMID:33753492
NCBI chr 4:139,464,357...139,560,841
Ensembl chr 4:139,464,373...139,560,839
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Paxbp1
PAX3 and PAX7 binding protein 1
IAGP
MGI
PMID:33753492
NCBI chr16:90,810,925...90,841,267
Ensembl chr16:90,810,925...90,841,431
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Pdss2
prenyl (solanesyl) diphosphate synthase, subunit 2
IAGP
MGI
PMID:18437205 PMID:23150520
NCBI chr10:43,095,396...43,340,878
Ensembl chr10:43,097,482...43,340,878
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Pex5
peroxisomal biogenesis factor 5
IAGP
MGI
PMID:15732085
NCBI chr 6:124,373,774...124,392,878
Ensembl chr 6:124,373,775...124,392,026
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Pink1
PTEN induced putative kinase 1
IAGP
MGI
PMID:19492057
NCBI chr 4:138,040,718...138,053,631
Ensembl chr 4:138,040,720...138,053,618
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Polg2
polymerase (DNA directed), gamma 2, accessory subunit
IAGP
MGI
PMID:23197651
NCBI chr11:106,659,030...106,670,363
Ensembl chr11:106,659,079...106,670,363
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Ppargc1b
peroxisome proliferative activated receptor, gamma, coactivator 1 beta
IAGP
MGI
PMID:24049736
NCBI chr18:61,424,516...61,533,846
Ensembl chr18:61,431,207...61,533,502
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Rnaseh1
ribonuclease H1
IAGP
MGI
PMID:12667461
NCBI chr12:28,699,600...28,709,591
Ensembl chr12:28,699,601...28,709,588
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Sdhb
succinate dehydrogenase complex, subunit B, iron sulfur (Ip)
IAGP
MGI
PMID:35472723
NCBI chr 4:140,688,582...140,706,509
Ensembl chr 4:140,688,514...140,706,504
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Sdhd
succinate dehydrogenase complex, subunit D, integral membrane protein
IAGP
MGI
PMID:15572694
NCBI chr 9:50,507,640...50,515,149
Ensembl chr 9:50,507,657...50,515,112
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Shmt2
serine hydroxymethyltransferase 2 (mitochondrial)
IAGP
MGI
PMID:29323231
NCBI chr10:127,352,992...127,358,313
Ensembl chr10:127,352,992...127,358,313
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Slc41a1
solute carrier family 41, member 1
IAGP
MGI
PMID:33153064
NCBI chr 1:131,755,236...131,776,601
Ensembl chr 1:131,755,231...131,776,603
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Slc6a3
solute carrier family 6 (neurotransmitter transporter, dopamine), member 3
IAGP
MGI
PMID:22914740
NCBI chr13:73,684,270...73,726,791
Ensembl chr13:73,684,866...73,726,791
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Snca
synuclein, alpha
IAGP
MGI
PMID:12376616
NCBI chr 6:60,708,557...60,806,839
Ensembl chr 6:60,708,559...60,806,839
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Sod2
superoxide dismutase 2, mitochondrial
IAGP
MGI
PMID:11226230 PMID:11514315
NCBI chr17:13,226,726...13,237,006
Ensembl chr17:13,225,733...13,258,950
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Spata19
spermatogenesis associated 19
IAGP
MGI
PMID:26265198
NCBI chr 9:27,308,103...27,313,007
Ensembl chr 9:27,308,096...27,313,081
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Speer6-ps1
spermatogenesis associated glutamate (E)-rich protein 6, pseudogene 1
IAGP
MGI
PMID:15732085 PMID:18437205 PMID:23847050 PMID:37524868
NCBI chr13:3,199,475...3,239,678
Ensembl chr13:3,236,206...3,239,317 Ensembl chr13:3,236,206...3,239,317
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Sqstm1
sequestosome 1
IAGP
MGI
PMID:22222206
NCBI chr11:50,090,979...50,105,303
Ensembl chr11:50,090,193...50,101,654
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Stmp1
short transmembrane mitochondrial protein 1
IAGP
MGI
PMID:35101990
NCBI chr 6:35,229,645...35,238,574
Ensembl chr 6:35,229,589...35,240,431
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Surf1
surfeit gene 1
IAGP
MGI
PMID:12566387
NCBI chr 2:26,803,390...26,806,667
Ensembl chr 2:26,803,393...26,806,542
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Taco1
translational activator of mitochondrially encoded cytochrome c oxidase I
IAGP
MGI
PMID:27319982
NCBI chr11:105,956,885...105,964,861
Ensembl chr11:105,956,887...105,964,438
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Tafazzin
tafazzin, phospholipid-lysophospholipid transacylase
IAGP
MGI
PMID:34129362
NCBI chr X:73,325,498...73,340,182
Ensembl chr X:73,325,518...73,333,757
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Tfam
transcription factor A, mitochondrial
IAGP
MGI
PMID:10737799 PMID:11062475 PMID:11259653 PMID:11588181 PMID:12417746
NCBI chr10:71,061,298...71,074,157
Ensembl chr10:71,061,294...71,074,110
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Tfb1m
transcription factor B1, mitochondrial
IAGP
MGI
PMID:19356719
NCBI chr17:3,569,119...3,608,064
Ensembl chr17:3,569,531...3,608,056
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Them5
thioesterase superfamily member 5
IAGP
MGI
PMID:22586271
NCBI chr 3:94,249,406...94,254,659
Ensembl chr 3:94,249,406...94,254,659
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Thrap3
thyroid hormone receptor associated protein 3
IAGP
MGI
PMID:37524868
NCBI chr 4:126,057,875...126,096,548
Ensembl chr 4:126,057,875...126,096,553
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Tmem135
transmembrane protein 135
IAGP
MGI
PMID:27863209
NCBI chr 7:88,789,230...89,053,911
Ensembl chr 7:88,788,922...89,053,430
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Trp53inp1
transformation related protein 53 inducible nuclear protein 1
IAGP
MGI
PMID:25828351
NCBI chr 4:11,156,441...11,174,379
Ensembl chr 4:11,156,431...11,174,379
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Twnk
twinkle mtDNA helicase
IAGP
MGI
PMID:23393161
NCBI chr19:44,994,102...45,001,203
Ensembl chr19:44,994,102...45,001,201
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Uqcc6
ubiquinol-cytochrome c reductase complex assembly factor 6
IAGP
MGI
PMID:35977508
NCBI chr10:82,455,685...82,459,062
Ensembl chr10:82,455,685...82,459,062
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Uqcrfs1
ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1
IAGP
MGI
PMID:22028811
NCBI chr13:30,724,295...30,729,299
Ensembl chr13:30,724,291...30,729,345
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Vdac3
voltage-dependent anion channel 3
IAGP
MGI
PMID:11507092
NCBI chr 8:23,067,091...23,083,829
Ensembl chr 8:23,067,102...23,083,774
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Ak1
adenylate kinase 1
IAGP
MGI
PMID:11101510
NCBI chr 2:32,511,770...32,525,070
Ensembl chr 2:32,511,770...32,525,070
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Cltrn
collectrin, amino acid transport regulator
IAGP
MGI
PMID:19246514
NCBI chr X:162,873,183...162,901,855
Ensembl chr X:162,871,826...162,901,856
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Cluh
clustered mitochondria homolog
IAGP
MGI
PMID:28188211
NCBI chr11:74,539,707...74,561,680
Ensembl chr11:74,540,321...74,561,673
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Crat
carnitine acetyltransferase
IAGP
MGI
PMID:22560225
NCBI chr 2:30,290,483...30,305,602
Ensembl chr 2:30,290,483...30,305,825
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Csl
citrate synthase like
IAGP
MGI
PMID:31857692
NCBI chr10:99,593,567...99,595,346
Ensembl chr10:99,593,568...99,595,520
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Fh1
fumarate hydratase 1
IAGP
MGI
PMID:23643539
NCBI chr 1:175,428,944...175,453,201
Ensembl chr 1:175,427,940...175,453,201
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Gpt2
glutamic pyruvate transaminase (alanine aminotransferase) 2
IAGP
MGI
PMID:27601654
NCBI chr 8:86,219,090...86,255,531
Ensembl chr 8:86,219,205...86,254,189
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Gt(ROSA)26Sor
gene trap ROSA 26, Philippe Soriano
IAGP
MGI
PMID:31469588
NCBI chr 6:113,044,389...113,054,205
Ensembl chr 6:113,043,843...113,055,336
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Lipa
lysosomal acid lipase A
IAGP
MGI
PMID:30639734
NCBI chr19:34,469,716...34,504,874
Ensembl chr19:34,469,718...34,504,874
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Mmut
methylmalonyl-Coenzyme A mutase
IAGP
MGI
PMID:19088183
NCBI chr17:41,245,576...41,272,880
Ensembl chr17:41,245,576...41,272,879
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Mterf2
mitochondrial transcription termination factor 2
IAGP
MGI
PMID:19490905
NCBI chr10:84,951,092...84,963,982
Ensembl chr10:84,955,297...84,963,891
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Park7
Parkinson disease (autosomal recessive, early onset) 7
IAGP
MGI
PMID:17766438
NCBI chr 4:150,981,590...150,994,378
Ensembl chr 4:150,981,590...150,998,894
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Pdx1
pancreatic and duodenal homeobox 1
IAGP
MGI
PMID:11781323
NCBI chr 5:147,206,907...147,212,658
Ensembl chr 5:147,206,769...147,212,658
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Ppargc1b
peroxisome proliferative activated receptor, gamma, coactivator 1 beta
IAGP
MGI
PMID:24049736
NCBI chr18:61,424,516...61,533,846
Ensembl chr18:61,431,207...61,533,502
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Sdhaf4
succinate dehydrogenase complex assembly factor 4
IAGP
MGI
PMID:35803927
NCBI chr 1:24,035,020...24,044,721
Ensembl chr 1:24,035,020...24,044,737
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Sdhc
succinate dehydrogenase complex, subunit C, integral membrane protein
IAGP
MGI
PMID:31469588
NCBI chr 1:170,956,726...170,978,209
Ensembl chr 1:170,954,734...170,978,172
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Slc41a1
solute carrier family 41, member 1
IAGP
MGI
PMID:33153064
NCBI chr 1:131,755,236...131,776,601
Ensembl chr 1:131,755,231...131,776,603
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Sod2
superoxide dismutase 2, mitochondrial
IAGP
MGI
PMID:7493016 PMID:9927656 PMID:11677043 PMID:15721992
NCBI chr17:13,226,726...13,237,006
Ensembl chr17:13,225,733...13,258,950
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Speer6-ps1
spermatogenesis associated glutamate (E)-rich protein 6, pseudogene 1
IAGP
MGI
PMID:27689697 PMID:30639734
NCBI chr13:3,199,475...3,239,678
Ensembl chr13:3,236,206...3,239,317 Ensembl chr13:3,236,206...3,239,317
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Trmu
tRNA 5-methylaminomethyl-2-thiouridylate methyltransferase
IAGP
MGI
PMID:27689697
NCBI chr15:85,763,505...85,781,595
Ensembl chr15:85,763,513...85,781,595
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Aifm1
apoptosis-inducing factor, mitochondrion-associated 1
IAGP
MGI
PMID:16917506
NCBI chr X:47,563,821...47,602,440
Ensembl chr X:47,563,821...47,602,440
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Foxg1
forkhead box G1
IAGP
MGI
PMID:16917506
NCBI chr12:49,429,666...49,433,650
Ensembl chr12:49,429,443...49,433,644
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Gt(ROSA)26Sor
gene trap ROSA 26, Philippe Soriano
IAGP
MGI
PMID:33753492
NCBI chr 6:113,044,389...113,054,205
Ensembl chr 6:113,043,843...113,055,336
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Mapk12
mitogen-activated protein kinase 12
IAGP
MGI
PMID:19936205
NCBI chr15:89,014,787...89,025,270
Ensembl chr15:89,014,787...89,024,906
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Pax7
paired box 7
IAGP
MGI
PMID:33753492
NCBI chr 4:139,464,357...139,560,841
Ensembl chr 4:139,464,373...139,560,839
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Paxbp1
PAX3 and PAX7 binding protein 1
IAGP
MGI
PMID:33753492
NCBI chr16:90,810,925...90,841,267
Ensembl chr16:90,810,925...90,841,431
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Tmem135
transmembrane protein 135
IAGP
MGI
PMID:27863209
NCBI chr 7:88,789,230...89,053,911
Ensembl chr 7:88,788,922...89,053,430
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Ucp2
uncoupling protein 2 (mitochondrial, proton carrier)
IAGP
MGI
PMID:15634780
NCBI chr 7:100,142,565...100,148,832
Ensembl chr 7:100,142,544...100,151,227
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A1cf
APOBEC1 complementation factor
IAGP
MGI
PMID:24658400
NCBI chr19:31,846,156...31,929,765
Ensembl chr19:31,846,164...31,926,395
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Adck2
aarF domain containing kinase 2
IAGP
MGI
PMID:31480808
NCBI chr 6:39,550,778...39,565,703
Ensembl chr 6:39,550,807...39,565,703
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Cox15
cytochrome c oxidase assembly protein 15
IAGP
MGI
PMID:21723506
NCBI chr19:43,721,693...43,741,439
Ensembl chr19:43,721,693...43,741,439
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Dnajc30
DnaJ heat shock protein family (Hsp40) member C30
IAGP
MGI
PMID:30318146
NCBI chr 5:135,093,060...135,094,219
Ensembl chr 5:135,093,056...135,094,716
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Fxn
frataxin
IAGP
MGI
PMID:11175786
NCBI chr19:24,236,909...24,257,954
Ensembl chr19:24,238,817...24,257,969
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Gt(ROSA)26Sor
gene trap ROSA 26, Philippe Soriano
IAGP
MGI
PMID:21068380
NCBI chr 6:113,044,389...113,054,205
Ensembl chr 6:113,043,843...113,055,336
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Lbr
lamin B receptor
IAGP
MGI
PMID:830768
NCBI chr 1:181,642,880...181,669,933
Ensembl chr 1:181,642,900...181,670,611
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Mfn1
mitofusin 1
IAGP
MGI
PMID:33674260
NCBI chr 3:32,583,594...32,633,384
Ensembl chr 3:32,583,614...32,633,388
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Mfn2
mitofusin 2
IAGP
MGI
PMID:33674260
NCBI chr 4:147,958,043...147,989,527
Ensembl chr 4:147,958,056...147,989,161
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mt-Nd6
NADH dehydrogenase 6, mitochondrial
IAGP
MGI
PMID:23129651
NCBI chr MT:13,552...14,070
Ensembl chr MT:13,552...14,070
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Prkaa1
protein kinase, AMP-activated, alpha 1 catalytic subunit
IAGP
MGI
PMID:21124450
NCBI chr15:5,172,641...5,211,380
Ensembl chr15:5,173,343...5,211,380
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Prkaa2
protein kinase, AMP-activated, alpha 2 catalytic subunit
IAGP
MGI
PMID:21124450
NCBI chr 4:104,886,846...104,967,095
Ensembl chr 4:104,887,071...104,967,087
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Slc25a3
solute carrier family 25 (mitochondrial carrier, phosphate carrier), member 3
IAGP
MGI
PMID:24658400
NCBI chr10:90,952,436...90,959,902
Ensembl chr10:90,952,436...90,959,921
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Stk11
serine/threonine kinase 11
IAGP
MGI
PMID:21124450
NCBI chr10:79,951,602...79,966,513
Ensembl chr10:79,951,637...79,966,516
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Surf1
surfeit gene 1
IAGP
MGI
PMID:21723506
NCBI chr 2:26,803,390...26,806,667
Ensembl chr 2:26,803,393...26,806,542
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Uqcrfs1
ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1
IAGP
MGI
PMID:22914734
NCBI chr13:30,724,295...30,729,299
Ensembl chr13:30,724,291...30,729,345
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