ONTOLOGY REPORT - ANNOTATIONS
Term: mitochondrion localization
Accession: GO:0051646
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Definition: Any process in which a mitochondrion or mitochondria are transported to, and/or maintained in, a specific location within the cell.
Synonyms: exact_synonym: establishment and maintenance of mitochondria localization; establishment and maintenance of mitochondrion localization; localization of mitochondria; localization of mitochondrion; mitochondria localization; mitochondrial localization; mitochondrion localisation
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Brat1
BRCA1-associated ATM activator 1
involved_in
ISO
(PMID:25070371)
RGD
PMID:25070371
NCBI chr12:19,043,004...19,065,686
Ensembl chr12:13,928,898...13,941,248
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Ehbp1l1
EH domain binding protein 1-like 1
acts_upstream_of_or_within
ISO
(PMID:37042948)
RGD
PMID:37042948
NCBI chr 1:212,423,444...212,444,357
Ensembl chr 1:202,994,118...203,014,270
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Hdac6
histone deacetylase 6
involved_in
ISO IEA
(PMID:20457763) GO_REF:0000107
RGD Ensembl
PMID:20457763
GO_REF:0000107
NCBI chr X:17,222,538...17,244,373
Ensembl chr X:14,551,044...14,572,441
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Lrrk2
leucine-rich repeat kinase 2
involved_in
ISO IEA
(PMID:22764206) GO_REF:0000107
RGD Ensembl
PMID:22764206
GO_REF:0000107
NCBI chr 7:124,706,246...124,867,234
Ensembl chr 7:122,826,696...122,987,703
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Mfn1
mitofusin 1
involved_in
IEA IBA ISO ISS
GO_REF:0000107 GO_REF:0000033 (PMID:12759376) GO_REF:0000024
Ensembl GO_Central RGD UniProt
PMID:12759376
GO_REF:0000024 GO_REF:0000033 GO_REF:0000107
NCBI chr 2:117,240,525...117,288,017
Ensembl chr 2:115,313,401...115,359,640
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Mfn2
mitofusin 2
involved_in
ISO IBA IEA
(PMID:11181170) GO_REF:0000033 GO_REF:0000107
RGD GO_Central Ensembl
PMID:11181170
GO_REF:0000033 GO_REF:0000107
NCBI chr 5:163,587,463...163,617,363
Ensembl chr 5:158,304,287...158,335,342
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Mul1
mitochondrial E3 ubiquitin protein ligase 1
involved_in
ISO IEA
(PMID:18213395) GO_REF:0000107
RGD Ensembl
PMID:18213395
GO_REF:0000107
NCBI chr 5:155,936,112...155,945,163
Ensembl chr 5:150,652,812...150,661,863
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Plin5
perilipin 5
involved_in
ISO IEA
(PMID:21885430) GO_REF:0000107
RGD Ensembl
PMID:21885430
GO_REF:0000107
NCBI chr 9:1,026,910...1,033,352
Ensembl chr 9:939,747...946,120
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Prkn
parkin RBR E3 ubiquitin protein ligase
involved_in
IDA
PMID:20457763
ParkinsonsUK-UCL
PMID:20457763
RGD:10047224
NCBI chr 1:51,236,410...52,430,242
Ensembl chr 1:48,690,556...49,882,555
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Stoml2
stomatin like 2
NOT|involved_in
ISO
(PMID:22623988)
RGD
PMID:22623988
NCBI chr 5:62,052,042...62,055,639
Ensembl chr 5:57,256,220...57,259,920
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Tle6
TLE family member 6, subcortical maternal complex member
involved_in
ISO
(PMID:28992324)
RGD
PMID:28992324
NCBI chr 7:8,757,846...8,769,405
Ensembl chr 7:8,107,207...8,118,639
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Zbed3
zinc finger, BED-type containing 3
involved_in
ISO
(PMID:28992324)
RGD
PMID:28992324
NCBI chr 2:28,323,968...28,334,910
Ensembl chr 2:26,587,572...26,600,386
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Agbl4
AGBL carboxypeptidase 4
acts_upstream_of_or_within
ISO
MGI:1918244 (PMID:30420556)
RGD
PMID:30420556
NCBI chr 5:130,483,551...131,762,906
Ensembl chr 5:125,254,956...126,534,367
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Agtpbp1
ATP/GTP binding carboxypeptidase 1
acts_upstream_of_or_within
ISO
MGI:1918244 (PMID:30420556)
RGD
PMID:30420556
NCBI chr17:5,092,108...5,244,414
Ensembl chr17:5,120,609...5,238,869
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Armcx3
armadillo repeat containing, X-linked 3
acts_upstream_of_or_within
ISO IEA
(PMID:22569362) GO_REF:0000107
RGD Ensembl
PMID:22569362
GO_REF:0000107
NCBI chr X:102,230,464...102,234,017
Ensembl chr X:97,936,999...97,942,098
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Hdac6
histone deacetylase 6
involved_in
IMP IEA ISO
GO_REF:0000107 UniProtKB:O75506 (PMID:28105056)
Ensembl RGD
PMID:28105056 PMID:22937007
GO_REF:0000107, RGD:9681555
NCBI chr X:17,222,538...17,244,373
Ensembl chr X:14,551,044...14,572,441
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Hif1a
hypoxia inducible factor 1 subunit alpha
involved_in
ISO IEA ISS
(PMID:19528298) GO_REF:0000107 GO_REF:0000024
RGD Ensembl UniProt
PMID:19528298
GO_REF:0000024 GO_REF:0000107
NCBI chr 6:98,357,788...98,405,068
Ensembl chr 6:92,624,390...92,669,261
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Hsbp1
heat shock factor binding protein 1
involved_in
ISO IEA
(PMID:28105056) GO_REF:0000107
RGD Ensembl
PMID:28105056
GO_REF:0000107
NCBI chr19:64,309,703...64,314,035
Ensembl chr19:47,400,966...47,435,821
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Map6
microtubule-associated protein 6
involved_in
IMP
PMID:28521134
UniProt
PMID:28521134
RGD:13441203
NCBI chr 1:162,980,339...163,046,548
Ensembl chr 1:153,568,368...153,634,414
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Mgarp
mitochondria-localized glutamic acid-rich protein
involved_in
ISO
(PMID:19528298)
RGD
PMID:19528298
NCBI chr 2:137,582,152...137,590,294
Ensembl chr 2:135,431,283...135,439,612
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Nefl
neurofilament light chain
involved_in
ISO IEA
(PMID:15857389) GO_REF:0000107
RGD Ensembl
PMID:15857389
GO_REF:0000107
NCBI chr15:46,477,330...46,481,203
Ensembl chr15:42,301,916...42,305,793
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Spast
spastin
involved_in
ISS ISO IEA
GO_REF:0000024 (PMID:19453301) GO_REF:0000107
UniProt RGD Ensembl
PMID:19453301
GO_REF:0000024 GO_REF:0000107
NCBI chr 6:26,807,220...26,858,456
Ensembl chr 6:21,055,349...21,107,954
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Sybu
syntabulin
involved_in
IMP IBA
GO_REF:0000033
GO_Central RGD
PMID:19828815
GO_REF:0000033, RGD:13217418
NCBI chr 7:77,731,662...77,833,413
Ensembl chr 7:75,847,003...75,948,828
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Trak1
trafficking kinesin protein 1
IMP
RGD
PMID:23395375
RGD:13208834
NCBI chr 8:129,861,967...130,016,870
Ensembl chr 8:120,984,431...121,139,367
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Uchl1
ubiquitin C-terminal hydrolase L1
acts_upstream_of_or_within
ISO IEA
MGI:1856882 (PMID:2558488) GO_REF:0000107
RGD Ensembl
PMID:2558488
GO_REF:0000107
NCBI chr14:41,838,859...41,849,743
Ensembl chr14:41,485,031...41,495,590
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Trak2
trafficking kinesin protein 2
IMP
RGD
PMID:23395375
RGD:13208834
NCBI chr 9:67,842,680...67,909,786
Ensembl chr 9:60,350,012...60,413,996
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Wasf1
WASP family member 1
involved_in
IDA IMP
PMID:18287015
SynGO
PMID:18287015 PMID:18287015
RGD:13702174 , RGD:13702174
NCBI chr20:45,908,458...45,956,118
Ensembl chr20:44,325,795...44,372,996
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Fez1
fasciculation and elongation protein zeta 1
IMP
RGD
PMID:17669366
RGD:2316312
NCBI chr 8:44,733,288...44,778,519
Ensembl chr 8:36,544,535...36,589,683
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Mark1
microtubule affinity regulating kinase 1
involved_in
IEA ISO
GO_REF:0000107 (PMID:18492799)
Ensembl RGD
PMID:18492799
GO_REF:0000107
NCBI chr13:98,981,727...99,086,998
Ensembl chr13:96,451,487...96,555,173
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Nectin2
nectin cell adhesion molecule 2
acts_upstream_of_or_within
ISO IEA
MGI:2183405 (PMID:10733589) GO_REF:0000107
RGD Ensembl
PMID:10733589
GO_REF:0000107
NCBI chr 1:88,500,086...88,535,474
Ensembl chr 1:79,372,119...79,407,360
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Rhot1
ras homolog family member T1
IMP
RGD
PMID:24302729
RGD:12904672
NCBI chr10:65,685,687...65,760,682
Ensembl chr10:65,170,560...65,262,804
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Armc1
armadillo repeat containing 1
involved_in
ISO IEA
(PMID:31644573) GO_REF:0000107
RGD Ensembl
PMID:31644573
GO_REF:0000107
NCBI chr 2:101,608,171...101,652,198
Ensembl chr 2:101,608,288...101,652,171
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Bhlha15
basic helix-loop-helix family, member a15
acts_upstream_of_or_within
ISO
MGI:2182768 (PMID:15665001)
RGD
PMID:15665001
NCBI chr12:15,534,123...15,538,299
Ensembl chr12:10,420,467...10,424,713
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Cluh
clustered mitochondria homolog
involved_in
ISO IBA
(PMID:25349259) GO_REF:0000033
RGD GO_Central
PMID:25349259
GO_REF:0000033
NCBI chr10:60,008,052...60,029,742
Ensembl chr10:59,509,726...59,531,345
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Dnm1l
dynamin 1-like
involved_in
IMP IBA ISO
GO_REF:0000033 (PMID:11514614)
GO_Central RGD
PMID:11514614 PMID:19605646
GO_REF:0000033, RGD:7800727
NCBI chr11:98,084,049...98,135,663
Ensembl chr11:84,581,216...84,631,482
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Kat2a
lysine acetyltransferase 2A
IMP
RGD
PMID:19542216
RGD:9590232
NCBI chr10:86,132,535...86,140,877
Ensembl chr10:85,632,216...85,640,166
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Lrrk2
leucine-rich repeat kinase 2
involved_in
ISO IEA
(PMID:21159966) GO_REF:0000107
RGD Ensembl
PMID:21159966
GO_REF:0000107
NCBI chr 7:124,706,246...124,867,234
Ensembl chr 7:122,826,696...122,987,703
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Mapt
microtubule-associated protein tau
involved_in
ISO
(PMID:21854751)
RGD
PMID:21854751
NCBI chr10:89,638,618...89,736,108
Ensembl chr10:89,138,627...89,236,129
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Mfn1
mitofusin 1
IMP
RGD
PMID:19605646
RGD:7800727
NCBI chr 2:117,240,525...117,288,017
Ensembl chr 2:115,313,401...115,359,640
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Mfn2
mitofusin 2
IMP
RGD
PMID:19605646
RGD:7800727
NCBI chr 5:163,587,463...163,617,363
Ensembl chr 5:158,304,287...158,335,342
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Ogt
O-linked N-acetylglucosamine (GlcNAc) transferase
IMP
RGD
PMID:24995978
RGD:9590184
NCBI chr X:70,811,317...70,856,123
Ensembl chr X:66,771,349...66,816,146
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Opa1
OPA1, mitochondrial dynamin like GTPase
involved_in
IMP IBA
GO_REF:0000033
GO_Central RGD
PMID:19605646
GO_REF:0000033, RGD:7800727
NCBI chr11:84,612,943...84,690,025
Ensembl chr11:71,109,873...71,185,109
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Synj2bp
synaptojanin 2 binding protein
IDA
via binding with Synj2_v3; recruits mitochondria to perinuclear region
RGD
PMID:10357812
RGD:69391
NCBI chr 6:106,920,970...106,958,653
Ensembl chr 6:101,189,714...101,227,406
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AABR07005775.1
involved_in
IEA
GO_REF:0000107
Ensembl
GO_REF:0000107
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Atp2a1
ATPase sarcoplasmic/endoplasmic reticulum Ca2+ transporting 1
involved_in
ISO IEA
(PMID:19061639) GO_REF:0000107
RGD Ensembl
PMID:19061639
GO_REF:0000107
NCBI chr 1:190,457,198...190,475,410
Ensembl chr 1:181,026,608...181,044,838
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Atcay
ATCAY kinesin light chain interacting caytaxin
involved_in
IMP
PMID:19861499
UniProt
PMID:19861499
RGD:5683640
NCBI chr 7:9,138,485...9,162,249
Ensembl chr 7:8,487,763...8,512,663
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Hap1
huntingtin-associated protein 1
involved_in
IBA
GO_REF:0000033
GO_Central
GO_REF:0000033
NCBI chr10:85,778,267...85,786,553
Ensembl chr10:85,277,890...85,286,126
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Mef2a
myocyte enhancer factor 2a
involved_in
ISO IEA
(PMID:12379849) GO_REF:0000107
RGD Ensembl
PMID:12379849
GO_REF:0000107
NCBI chr 1:130,258,083...130,392,819
Ensembl chr 1:120,850,080...120,981,948
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Msto1
misato mitochondrial distribution and morphology regulator 1
involved_in
ISO IEA
(PMID:17349998) GO_REF:0000107
RGD Ensembl
PMID:17349998
GO_REF:0000107
NCBI chr 2:176,603,755...176,608,037
Ensembl chr 2:174,301,861...174,310,216
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Mtm1
myotubularin 1
involved_in acts_upstream_of_or_within
ISO IBA ISS
(PMID:21135508) MGI:2450992 (PMID:18434328) GO_REF:0000033 GO_REF:0000024
RGD GO_Central UniProt
PMID:18434328 PMID:21135508
GO_REF:0000024 GO_REF:0000033
NCBI chr 6:6,234,917...6,252,874
Ensembl chr 6:488,969...506,860
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Slc4a5
solute carrier family 4 member 5
acts_upstream_of_or_within
ISO
(PMID:21705333)
RGD
PMID:21705333
NCBI chr 4:117,267,803...117,368,024
Ensembl chr 4:115,725,592...115,810,323
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Trak1
trafficking kinesin protein 1
involved_in
IBA
GO_REF:0000033
GO_Central
GO_REF:0000033
NCBI chr 8:129,861,967...130,016,870
Ensembl chr 8:120,984,431...121,139,367
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Trak2
trafficking kinesin protein 2
involved_in
IBA
GO_REF:0000033
GO_Central
GO_REF:0000033
NCBI chr 9:67,842,680...67,909,786
Ensembl chr 9:60,350,012...60,413,996
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Myo19
myosin XIX
acts_upstream_of_or_within
ISO
(PMID:19932026)
RGD
PMID:19932026
NCBI chr10:70,250,500...70,279,867
Ensembl chr10:69,753,068...69,782,450
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Kif1b
kinesin family member 1B
acts_upstream_of_or_within involved_in
ISO IEA ISS
(PMID:7528108) GO_REF:0000107 GO_REF:0000024 (PMID:16225668)
RGD Ensembl UniProt
PMID:7528108 PMID:16225668
GO_REF:0000024 GO_REF:0000107
NCBI chr 5:164,890,778...165,025,848
Ensembl chr 5:159,561,271...159,742,778
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Kif5b
kinesin family member 5B
acts_upstream_of_or_within
ISO IEA
(PMID:34048705) GO_REF:0000107
RGD Ensembl
PMID:34048705
GO_REF:0000107
NCBI chr17:56,185,386...56,222,990
Ensembl chr17:51,489,944...51,527,508
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Kifbp
kinesin family binding protein
involved_in
ISO IEA ISS
(PMID:16225668) GO_REF:0000107 GO_REF:0000024
RGD Ensembl UniProt
PMID:16225668
GO_REF:0000024 GO_REF:0000107
NCBI chr20:31,055,625...31,075,232
Ensembl chr20:30,512,901...30,532,476
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Map1b
microtubule-associated protein 1B
acts_upstream_of_or_within
ISO IEA
MGI:2148182 (PMID:16536727) GO_REF:0000107
RGD Ensembl
PMID:16536727
GO_REF:0000107
NCBI chr 2:32,551,423...32,644,471
Ensembl chr 2:30,817,261...30,910,317
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Mapt
microtubule-associated protein tau
acts_upstream_of_or_within
ISO
MGI:2385630 (PMID:16536727)
RGD
PMID:16536727
NCBI chr10:89,638,618...89,736,108
Ensembl chr10:89,138,627...89,236,129
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Pgd
phosphogluconate dehydrogenase
acts_upstream_of_or_within
IEA
GO_REF:0000107
Ensembl
GO_REF:0000107
NCBI chr 5:164,865,830...164,882,029
Ensembl chr 5:159,561,271...159,742,778
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Rhot1
ras homolog family member T1
involved_in
ISO
(PMID:16630562)
RGD
PMID:16630562
NCBI chr10:65,685,687...65,760,682
Ensembl chr10:65,170,560...65,262,804
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Rhot2
ras homolog family member T2
involved_in
ISO IBA ISS
(PMID:16630562) GO_REF:0000033 GO_REF:0000024
RGD GO_Central UniProt
PMID:16630562
GO_REF:0000024 GO_REF:0000033
NCBI chr10:15,363,467...15,369,263
Ensembl chr10:14,858,956...14,864,751
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Ubb
ubiquitin B
acts_upstream_of_or_within
ISO IEA
(PMID:17571083) GO_REF:0000107
RGD Ensembl
PMID:17571083
GO_REF:0000107
NCBI chr10:47,746,923...47,748,628
Ensembl chr10:47,245,637...47,249,333
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Dnm1l
dynamin 1-like
acts_upstream_of_or_within
ISO IEA
(PMID:34048705) GO_REF:0000107
RGD Ensembl
PMID:34048705
GO_REF:0000107
NCBI chr11:98,084,049...98,135,663
Ensembl chr11:84,581,216...84,631,482
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Dynll1
dynein light chain LC8-type 1
acts_upstream_of_or_within
ISO
(PMID:34048705)
RGD
PMID:34048705
NCBI chr12:46,945,291...46,976,867
Ensembl chr12:41,312,367...41,314,741
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Epcip
exosomal polycystin 1 interacting protein
involved_in
ISO IBA IEA
(PMID:37681898) GO_REF:0000033 GO_REF:0000107
RGD GO_Central Ensembl
PMID:37681898
GO_REF:0000033 GO_REF:0000107
NCBI chr11:43,793,924...43,811,388
Ensembl chr11:30,310,350...30,325,439
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Kif5b
kinesin family member 5B
acts_upstream_of_or_within
ISO IEA
(PMID:34048705) GO_REF:0000107
RGD Ensembl
PMID:34048705
GO_REF:0000107
NCBI chr17:56,185,386...56,222,990
Ensembl chr17:51,489,944...51,527,508
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Myo19
myosin XIX
acts_upstream_of_or_within
ISO IEA
(PMID:34048705) GO_REF:0000107
RGD Ensembl
PMID:34048705
GO_REF:0000107
NCBI chr10:70,250,500...70,279,867
Ensembl chr10:69,753,068...69,782,450
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Pkd1
polycystin 1, transient receptor potential channel interacting
involved_in
ISO IEA
(PMID:37681898) GO_REF:0000107
RGD Ensembl
PMID:37681898
GO_REF:0000107
NCBI chr10:14,077,733...14,125,682
Ensembl chr10:13,573,021...13,621,128
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Tspan4
tetraspanin 4
acts_upstream_of_or_within
ISO
(PMID:34048705)
RGD
PMID:34048705
NCBI chr 1:206,001,731...206,021,414
Ensembl chr 1:196,572,228...196,617,448
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Tspan9
tetraspanin 9
acts_upstream_of_or_within
ISO
MGI:6719497 (PMID:34048705)
RGD
PMID:34048705
NCBI chr 4:162,500,029...162,681,699
Ensembl chr 4:160,813,879...160,995,501
G
Fez1
fasciculation and elongation protein zeta 1
IMP
RGD
PMID:17173861
RGD:13208824
NCBI chr 8:44,733,288...44,778,519
Ensembl chr 8:36,544,535...36,589,683
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Actr10
actin related protein 10
involved_in
IBA
GO_REF:0000033
GO_Central
GO_REF:0000033
NCBI chr 6:95,182,082...95,208,325
Ensembl chr 6:89,446,093...89,473,047
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Agbl4
AGBL carboxypeptidase 4
acts_upstream_of_or_within
ISO
MGI:1918244 (PMID:30420556)
RGD
PMID:30420556
NCBI chr 5:130,483,551...131,762,906
Ensembl chr 5:125,254,956...126,534,367
G
Agtpbp1
ATP/GTP binding carboxypeptidase 1
acts_upstream_of_or_within
ISO
MGI:1918244 (PMID:30420556)
RGD
PMID:30420556
NCBI chr17:5,092,108...5,244,414
Ensembl chr17:5,120,609...5,238,869
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